Evans Erica, Nascene David, Sommer Katherine, Moertel Christopher
University of Minnesota Medical School, Minneapolis, MN, USA.
Department of Radiology, University of Minnesota Medical School, Minneapolis, MN, USA.
Child Neurol Open. 2019 Aug 6;6:2329048X19866617. doi: 10.1177/2329048X19866617. eCollection 2019.
The authors present 2 cases of cross-innervation in patients with neurofibromatosis type 2. In the first case, an iodine test was performed to demonstrate Frey syndrome in a 28-year-old female with neurofibromatosis type 2 who developed symptoms at age 10 years. The second patient is an 18-year-old female with neurofibromatosis type 2, 2 years status post left vestibular schwannoma subtotal resection who presented with paradoxical unilateral lacrimation and rhinorrhea triggered by heat stress and exercise. The pathophysiology of these cases is discussed.
作者报告了2例2型神经纤维瘤病患者的交叉神经支配情况。第一例中，对一名28岁、10岁起病的2型神经纤维瘤病女性患者进行了碘试验以证实存在弗雷综合征。第二例患者是一名18岁的2型神经纤维瘤病女性，在左侧前庭神经鞘瘤次全切除术后2年，出现由热应激和运动引发的矛盾性单侧流泪和鼻溢，文中讨论了这些病例的病理生理学。
