Guisasola F J, González H, del Real M, Valbuena C C, Peral I
Departamento de Pediatría, Facultad de Medicina, Valladolid.
An Esp Pediatr. 1988 May;28(5):455-8.
A case of cystic angiomatosis of bone without visceral involvement is presented. Lesions were noted in: skull, ribs, pelvis, long bones and phalanges. Besides clinical and radiological findings, the case, associates pancytopenia and coagulation disorders. The possibility of a bone marrow failure due to invasion of marrow by cystic angiomas and localized intravascular coagulation are discussed as cause of hematologic alterations.
本文报告一例无内脏受累的骨囊性血管瘤病病例。病变见于:颅骨、肋骨、骨盆、长骨和指骨。除临床和放射学表现外,该病例还伴有全血细胞减少和凝血障碍。文中讨论了囊性血管瘤侵犯骨髓导致骨髓衰竭以及局部血管内凝血作为血液学改变原因的可能性。