Gallardo-Rincón Dolores, Álvarez-Gómez Rosa María, Montes-Servín Edgar, Toledo-Leyva Alfredo, Montes-Servín Elizabeth, Michel-Tello David, Alamilla-García Gabriela, Bahena-González Antonio, Hernández-Nava Elizabeth, Fragoso-Ontiveros Veronica, Espinosa-Romero Raquel, Cetina-Pérez Lucely
Ovarian Cancer Program, Instituto Nacional de Cancerología, Mexico City, Mexico; Department of Medical Oncology, Instituto Nacional de Cancerología, Mexico City, Mexico.
Hereditary Cancer Clinic, Instituto Nacional de Cancerología, Mexico City, Mexico.
Transl Oncol. 2020 Feb;13(2):212-220. doi: 10.1016/j.tranon.2019.11.003. Epub 2019 Dec 20.
Ovarian cancer (OC) is an important cause of gynecologic cancer-related deaths. In Mexico, around 4700 new cases of OC are diagnosed per year and it represents the second cause of gynecological cancer mortality with more than 2700 deaths. Germline mutations in BRCA1/2 genes are present in 13-18% of OC cases. Few studies have evaluated the presence of mutations in BRCA genes in a population of OC Mexican patients and their relationship with clinical response and survival rates. A total of 179 OC patients were studied by molecular testing for BRCA1/2 through next-generation sequencing and multiplex ligation-dependent probe amplification. Recurrence-free survival (RFS) was estimated by the Kaplan-Meier method. BRCA mutation was detected in 33% of patients. A percentage of 66.1% were BRCA1 mutated and 33.9% were BRCA2 mutated. BRCA1 mutation carriers had a worst RFS compared with BRCA2 mutation carriers (37.6 [29-46.2] vs 72.7 [38.4-107.2]; P = 0.030). The most common mutation for BRCA1 was ex9-12del (28.2%) (Mexican founder mutation). The Mexican founder mutation had a better RFS than other BRCA1 mutations (86.1 [37.2-135.1] vs 34.5 [20.7-48.2]; P = 0.033). The presence of BRCA2 mutations in the ovarian cancer cluster region (OCCR) had a significantly better RFS than mutations in breast cancer cluster regions (BCCR) and not-related risk region (NRR) (NR vs 72.8 [39-106.6] vs 25.8 [8.3-43.2]; P = 0.013). These results demonstrate that the prevalence of BRCA1/2 positive patients in OC Mexican patients are the highest reported. Patients with mutations in BRCA2 have a better prognosis than those mutated in BRCA1. The Mexican founder mutation has an important role in clinical outcomes. These results highlight the importance to test all the HGSP (high-grade serous papillary) OC patients with or without cancer family history (CFH) in Mexican population.
卵巢癌(OC)是妇科癌症相关死亡的重要原因。在墨西哥,每年约有4700例新的OC病例被诊断出来,它是妇科癌症死亡的第二大原因,死亡人数超过2700人。BRCA1/2基因的种系突变存在于13%至18%的OC病例中。很少有研究评估墨西哥OC患者群体中BRCA基因的突变情况及其与临床反应和生存率的关系。通过下一代测序和多重连接依赖探针扩增对179例OC患者进行了BRCA1/2的分子检测。采用Kaplan-Meier方法估计无复发生存期(RFS)。33%的患者检测到BRCA突变。66.1%为BRCA1突变,33.9%为BRCA2突变。与BRCA2突变携带者相比,BRCA1突变携带者的RFS更差(37.6 [29 - 46.2] 对比 72.7 [38.4 - 107.2];P = 0.030)。BRCA1最常见的突变是ex9 - 12del(28.2%)(墨西哥始祖突变)。墨西哥始祖突变的RFS比其他BRCA1突变更好(86.1 [37.2 - 135.1] 对比 34.5 [20.7 - 48.2];P = 0.033)。卵巢癌簇区域(OCCR)中存在BRCA2突变的患者的RFS明显优于乳腺癌簇区域(BCCR)和非相关风险区域(NRR)中的突变患者(NR对比72.8 [39 - 106.6]对比25.8 [8.3 - 43.2];P = 0.013)。这些结果表明,墨西哥OC患者中BRCA1/2阳性患者的患病率是所报道的最高水平。BRCA2突变患者的预后比BRCA1突变患者更好。墨西哥始祖突变在临床结果中具有重要作用。这些结果凸显了对墨西哥人群中所有有或没有癌症家族史(CFH)的高级别浆液性乳头状(HGSP)OC患者进行检测的重要性。