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综合征型听力损失的颞骨和颅内异常:最新指南。

Temporal bone and intracranial abnormalities in syndromic causes of hearing loss: an updated guide.

机构信息

Department of Neuroradiology, Great Ormond Street Hospital for Children, London, UK.

Department of Neuroradiology, University College of London, London, UK.

出版信息

Eur J Radiol. 2020 Feb;123:108803. doi: 10.1016/j.ejrad.2019.108803. Epub 2019 Dec 26.

DOI:10.1016/j.ejrad.2019.108803
PMID:31891841
Abstract

PURPOSE

To describe in detail the temporal bone and brain findings in both common and rare syndromic causes of hearing loss, with the purpose of broadening among radiologists and enhance the current understanding of distinct imaging features in paediatric patients with syndromic hearing loss.

METHODS

A detailed search of electronic databases has been conducted, including PubMed, Ovid Medline, Scopus, Cochrane Library, Google Scholar, National Institute for Health and Care Excellence (NICE), Embase, and PsycINFO.

RESULTS

Syndromic causes of hearing loss are characterised by different and sometimes specific abnormalities in the temporal bone.

CONCLUSION

A complete knowledge of the image findings in the temporal bones, brain, skull and other body regions is critical for the optimal assessment and management of these patients.

摘要

目的

详细描述常见和罕见综合征性听力损失病因的颞骨和脑部发现,目的在于拓宽放射科医生的知识面,并增强对综合征性听力损失患儿的不同影像学特征的现有认识。

方法

对电子数据库进行了详细的搜索,包括 PubMed、Ovid Medline、Scopus、Cochrane Library、Google Scholar、英国国家卫生与保健优化研究所(NICE)、Embase 和 PsycINFO。

结果

综合征性听力损失的病因表现为颞骨的不同且有时是特定的异常。

结论

全面了解颞骨、脑部、颅骨和其他身体区域的影像学发现,对于这些患者的最佳评估和管理至关重要。

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