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表现为全垂体功能减退的神经结节病。

Neurosarcoidosis manifesting as panhypopituitarism.

作者信息

Oye Monique, Chahin Michael, Krishnan Nithya, Reddy Pramod

机构信息

Division of Internal Medicine Department of Medicine University of Florida College of Medicine Jacksonville Florida.

出版信息

Clin Case Rep. 2019 Nov 11;7(12):2472-2475. doi: 10.1002/ccr3.2521. eCollection 2019 Dec.

DOI:10.1002/ccr3.2521
PMID:31893082
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC6935632/
Abstract

Panhypopituitarism secondary to Neurosarcoidosis is a rare however serious complication. This diagnosis should remain in the differential in patients with hypothalamic-pituitary dysfunction. Biopsy of lesions will give definitive diagnosis.

摘要

继发于神经结节病的全垂体功能减退是一种罕见但严重的并发症。对于下丘脑-垂体功能障碍的患者,该诊断应保留在鉴别诊断范围内。病变活检将给出明确诊断。

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An Update on Advances in Hypopituitarism: Etiology, Diagnosis, and Current Management.垂体功能减退症的进展更新:病因、诊断及当前治疗
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本文引用的文献

1
Definition and Consensus Diagnostic Criteria for Neurosarcoidosis: From the Neurosarcoidosis Consortium Consensus Group.神经结节病的定义和共识诊断标准:来自神经结节病共识组。
JAMA Neurol. 2018 Dec 1;75(12):1546-1553. doi: 10.1001/jamaneurol.2018.2295.
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DIAGNOSIS OF ENDOCRINE DISEASE: Expanding the cause of hypopituitarism.内分泌疾病的诊断:扩大垂体功能减退的病因
Eur J Endocrinol. 2017 Jun;176(6):R269-R282. doi: 10.1530/EJE-16-1065. Epub 2017 Mar 3.
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Neurosarcoidosis: a clinical approach to diagnosis and management.神经结节病:诊断与管理的临床方法
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Clinical features, treatment and outcome in neurosarcoidosis: systematic review and meta-analysis.神经结节病的临床特征、治疗及预后:系统评价与荟萃分析
BMC Neurol. 2016 Nov 15;16(1):220. doi: 10.1186/s12883-016-0741-x.
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Hypopituitarism.垂体功能减退症
Lancet. 2016 Nov 12;388(10058):2403-2415. doi: 10.1016/S0140-6736(16)30053-8. Epub 2016 Mar 31.
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The hypothalamus.下丘脑。
Curr Biol. 2014 Dec 1;24(23):R1111-6. doi: 10.1016/j.cub.2014.10.023.
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The WASOG Sarcoidosis Organ Assessment Instrument: An update of a previous clinical tool.WASOG结节病器官评估工具:既往临床工具的更新
Sarcoidosis Vasc Diffuse Lung Dis. 2014 Apr 18;31(1):19-27.
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Neurosarcoidosis: clinical review of a disorder with challenging inpatient presentations and diagnostic considerations.神经结节病:一种具有挑战性的住院表现及诊断考量疾病的临床综述
Neurohospitalist. 2014 Apr;4(2):94-101. doi: 10.1177/1941874413519447.
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Hypothalamo-pituitary sarcoidosis: a multicenter study of 24 patients.下丘脑-垂体结节病:24 例患者的多中心研究。
QJM. 2012 Oct;105(10):981-95. doi: 10.1093/qjmed/hcs121. Epub 2012 Jun 30.
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The role of the hypothalamic-pituitary-adrenal axis in neuroendocrine responses to stress.下丘脑-垂体-肾上腺轴在应激神经内分泌反应中的作用。
Dialogues Clin Neurosci. 2006;8(4):383-95. doi: 10.31887/DCNS.2006.8.4/ssmith.