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特发性脉络膜新生血管性色素性视网膜炎中厚脉络膜新生血管的扫频源光学相干断层扫描血管造影研究。

SWEPT-SOURCE OPTICAL COHERENCE TOMOGRAPHY ANGIOGRAPHY FINDINGS IN A CASE OF PACHYCHOROID NEOVASCULOPATHY IN RETINITIS PIGMENTOSA.

机构信息

Department of Ophthalmology, IRCCS Ospedale Sacro Cuore Don Calabria, Negrar, Italy.

出版信息

Retin Cases Brief Rep. 2022 May 1;16(3):300-304. doi: 10.1097/ICB.0000000000000962. Epub 2020 Jan 6.

DOI:10.1097/ICB.0000000000000962
PMID:31913216
Abstract

PURPOSE

To report a rare case of pachychoroid neovasculopathy in retinitis pigmentosa (RP) and to describe its features and changes after treatment with bevacizumab as documented by swept-source optical coherence angiography.

METHODS

A case report of a 69-year-old man with a history of RP who presented at our clinic with an acute decrease in visual acuity (Best corrected visual acuity) in his left eye.

RESULTS

Upon the first examination, best-corrected visual acuity in the left eye was 20/50. Fundus examination and fundus autofluorescence showed bilaterally typical features of RP, and enhanced depth imaging-optical coherence tomography revealed a pachychoroid pattern. Fluorescein angiography and indocyanine green angiography suggested the presence of a choroidal neovascularization in the left eye, although no clear evidence of any neovascular network could be identified. Swept-source optical coherence angiography was performed, confirming the presence of a choroidal neovascularization network. The patient was treated with 2 monthly intravitreal injections of bevacizumab. After treatment, BVCA improved to 20/25, and no evidence of the vascular network was detectable on swept-source optical coherence angiography.

CONCLUSION

Our case reports the uncommon association of RP with pachychoroid neovasculopathy. Swept-source optical coherence angiography proved to be a useful imaging technique for the diagnosis and follow-up of this condition. Intravitreal bevacizumab represents an effective treatment for choroidal neovascularization associated with RP.

摘要

目的

报告一例罕见的色素性视网膜炎(RP)伴肥厚脉络膜新生血管病变,并描述其特征以及在接受贝伐单抗治疗后的变化,该变化通过扫频源光相干断层血管造影(SS-OCTA)得到证实。

方法

报告一名 69 岁男性病例,他有 RP 病史,因左眼视力急剧下降(最佳矫正视力)就诊于我院。

结果

左眼最佳矫正视力首次检查时为 20/50。眼底检查和眼底自发荧光显示双眼均具有典型的 RP 特征,增强深度成像光学相干断层扫描(EDI-OCT)显示为肥厚脉络膜。荧光素血管造影和吲哚青绿血管造影提示左眼存在脉络膜新生血管,但没有明确的新生血管网络证据。进行扫频源光相干断层血管造影检查,证实存在脉络膜新生血管网络。该患者接受了 2 个月每月一次的玻璃体腔内注射贝伐单抗治疗。治疗后,BVCA 提高到 20/25,并且在 SS-OCTA 上未检测到血管网络的证据。

结论

本病例报告了罕见的 RP 合并肥厚脉络膜新生血管病变。扫频源光相干断层血管造影术被证明是一种用于诊断和随访该疾病的有用成像技术。玻璃体内注射贝伐单抗是治疗与 RP 相关的脉络膜新生血管的有效方法。

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