Telich-Tarriba José E, Cárdenas-Mejía Alexander
Servicio de Cirugía Plástica y Reconstructiva, División de Cirugía Plástica y Reconstructiva, Hospital General Dr. Manuel Gea González. Ciudad de México, México.
División de Estudios de Posgrado, Universidad Nacional Autónoma de México. Ciudad de México, México.
Cir Cir. 2020;88(1):71-75. doi: 10.24875/CIRU.19000999.
Moebius syndrome is a clinical entity characterized by bilateral facial and abducens nerve palsies; other cranial nerver might be affected as well. So far, no studies have reported the electromyographic responses of the facial musculature in this group of patients.
The objective of our study is to describe the electromyographic responses of the facial muscle and the main donor nerves for facial reanimation in patients with Moebius syndrome.
We analyzed electromyographies from the facial, hypoglossal, masseterine (trigeminal) and accessory nerves from patients with Moebius syndrome treated between 2010 and 2016. Results are presented as percentages and central tendency measures.
24 patients were included, mean age 11.79 ± 9.39 years. The facial nerve showed complete unilateral recruitment in 4 patients, partial bilaterally in 11, 7 showed no activity bilaterally and two had unilateral inactivity. The masseterine was normal in 14 patients, had partial recruitment bilaterally in 4 and unilaterally in 4 cases. The accessory nerve was normal in 20 patients, showed partial recruitment bilaterally in 3 and unilaterally in 1 patients. The hypoglossal was normal in 22 patients, and altered in 2 cases.
Patients with Moebius syndrome show several degrees of alteration in electromyographic evaluation of the facial nerve. Electromyography is a useful tool in evaluating potential motor donor nerves for facial reanimation surgery.
梅比厄斯综合征是一种以双侧面部及展神经麻痹为特征的临床病症；其他颅神经也可能受到影响。迄今为止，尚无研究报道该组患者面部肌肉的肌电图反应。
我们研究的目的是描述梅比厄斯综合征患者面部肌肉以及用于面部重建的主要供体神经的肌电图反应。
我们分析了2010年至2016年期间接受治疗的梅比厄斯综合征患者的面部、舌下、咬肌（三叉神经）和副神经的肌电图。结果以百分比和集中趋势指标呈现。
纳入24例患者，平均年龄11.79±9.39岁。面神经在4例患者中显示完全单侧募集，11例双侧部分募集，7例双侧无活动，2例单侧无活动。咬肌在14例患者中正常，4例双侧部分募集，4例单侧募集。副神经在20例患者中正常，3例双侧部分募集，1例单侧募集。舌下神经在22例患者中正常，2例异常。
梅比厄斯综合征患者在面神经肌电图评估中表现出不同程度的改变。肌电图是评估面部重建手术潜在运动供体神经的有用工具。
