Nemeth Attila, Schlensak Christian, Popov Aron
Department of Thoracic and Cardiovascular Surgery, University Medical Center Tuebingen, Tuebingen, Germany.
J Card Surg. 2020 Mar;35(3):700-702. doi: 10.1111/jocs.14440. Epub 2020 Jan 25.
Cardiac paragangliomas are rare tumors that develop from neural crest cells. They account for about 2% of all paragangliomas and there is only limited evidence of malignant transformation.
We present a young woman with atypical symptoms, which are related to the mass effect of the 40 × 49mm cardiac tumor on top of the left atrium. The patient underwent an extensive resection of the tumor including the root of the pulmonary trunk, the ascending aorta, and the left main artery.
The present case is of great importance showing the need for multidisciplinary approach in the management of cardiac tumors that infiltrate multiple anatomic structures.
心脏副神经节瘤是起源于神经嵴细胞的罕见肿瘤。它们约占所有副神经节瘤的2%,恶性转化的证据有限。
我们报告一名年轻女性,其出现非典型症状,这与位于左心房上方的40×49mm心脏肿瘤的占位效应有关。患者接受了肿瘤广泛切除术,包括肺动脉干根部、升主动脉和左主动脉。
本病例非常重要,表明在处理浸润多个解剖结构的心脏肿瘤时需要多学科方法。