Alnefaie Nada, Alharbi Ahoud, Alamer Othman Bin, Khairy Ibtesam, Khairy Sami, Saeed Mahfood Abdullah, Azzubi Moutasem
College of Medicine, Kind Saud bin Abdulaziz University for Health Sciences, Riyadh, Saudi Arabia; King Abdullah International Medical Research Center, Riyadh, Saudi Arabia.
College of Medicine, Kind Saud bin Abdulaziz University for Health Sciences, Riyadh, Saudi Arabia; King Abdullah International Medical Research Center, Riyadh, Saudi Arabia.
World Neurosurg. 2020 Apr;136:e601-e607. doi: 10.1016/j.wneu.2020.01.092. Epub 2020 Jan 22.
Split cord malformation (SCM) is a rare anomaly characterized by a split along the midline of the cord, which divides it into 2 symmetric or nonsymmetric entities. SCM surgical indications and outcomes are still debatable, the signs and symptoms are generally nonspecific and are commonly associated with other anomalies and deficits.
We retrospectively searched the hospital database at King Abdulaziz Medical City, Riyadh, Saudi Arabia for patients with SCM between 1998 and 2018. Descriptive statistics were used to present categorical data as percentages and frequencies.
A total of 25 patients were included in this series. The mean age of patients at the time of diagnosis was 4.4 years. A total of 18 patients (72%) underwent surgical correction. The mean difference between the age at diagnosis and the age at correction was 7 months. All patients underwent intraoperative neurophysiologic monitoring. Postoperative complications were minimal. Cerebrospinal fluid leakage was noted in 2 patients, transient urinary retention was noted in 1 patient, and transient unilateral leg paresis was noted in 1 patient. Most patients (n = 15, 83%), were discharged within 19 days after surgery, and 81% showed improvement postoperatively. Over the long-term follow-up, none of the patients developed new urologic or neurologic deficits.
Most patients with SCM present during childhood. Postoperative complications after SCM corrective surgery are generally minimal, and the overall outcomes, mainly including partial or complete symptomatic improvement and/or symptom stability and hydronephrosis resolution, were favorable.
脊髓纵裂畸形（SCM）是一种罕见的异常情况，其特征是脊髓沿中线分裂，将其分为两个对称或不对称的部分。SCM的手术指征和结果仍存在争议，其体征和症状通常不具有特异性，且常与其他异常和缺陷相关。
我们回顾性检索了沙特阿拉伯利雅得阿卜杜勒阿齐兹国王医疗城的医院数据库，以查找1998年至2018年间患有SCM的患者。描述性统计用于将分类数据表示为百分比和频率。
本系列共纳入25例患者。诊断时患者的平均年龄为4.4岁。共有18例患者（72%）接受了手术矫正。诊断年龄与矫正年龄之间的平均差异为7个月。所有患者均接受了术中神经生理监测。术后并发症极少。2例患者出现脑脊液漏，1例患者出现短暂性尿潴留，1例患者出现短暂性单侧腿部轻瘫。大多数患者（n = 15，83%）在术后19天内出院，81%的患者术后病情有所改善。在长期随访中，没有患者出现新的泌尿系统或神经系统缺陷。
大多数SCM患者在儿童期发病。SCM矫正手术后的术后并发症通常极少，总体结果良好，主要包括部分或完全的症状改善和/或症状稳定以及肾积水消退。
