Scarpelli Daphne B, Turina Claire B, Kelly Patrick D, Khudanyan Arpine, Jaboin Jerry J, McClelland Shearwood
Department of Radiation Medicine, Oregon Health & Science University, 3181 SW Sam Jackson Park Rd, KPV4, Portland, OR 97239, USA.
Department of Neurological Surgery, Vanderbilt University Medical Center, 1161 21st Ave, T4224 Medical Center North, Nashville, TN 37232-2380, USA.
J Clin Neurosci. 2020 Mar;73:162-167. doi: 10.1016/j.jocn.2019.12.049. Epub 2020 Jan 24.
Myxopapillary ependymomas (MPE) are WHO Grade I ependymomas that annually occur in 0.05-0.08 per 100,000 people. Surgical resection is the recommended first line therapy. Due to the rarity of the disease, there is a relatively poor understanding of the use of radiotherapy (RT) in managing this disease. The National Cancer Database (NCDB) was analyzed for patterns of care foradult MPE diagnosed between 2002 and 2016. Of 753 qualifying cases, the majority of patients underwent resection (n = 617, 81.9%). A relatively small portion received RT (n = 103, 13.3%) with most receiving RT post-operatively (n = 98, 95.1%). The likelihood of patients to undergo resection and RT was associated with patient age at diagnosis (p = 0.002), tumor size (p < 0.001), and race (p = 0.017). Chemotherapy was not widely utilized (0.27% of patients). One limitation of our analysis is that there was no data on progression free survival (PFS), an important outcome given the high survival rate in this disease. Surgery remains the primary means to manage adult MPE. For spinal MPE, it is understood that gross total resection (GTR) should be attempted whenever possible as GTR has been associated with improved PFS in several studies. The impact of RT on overall survival (OS) is indeterminate given the 1.6% death rate in the cohort. Analyses of the impact of RT on PFS in a larger database would be beneficial for determining an algorithm for post-operative and definitive RT in this disease entity.
黏液乳头型室管膜瘤(MPE)是世界卫生组织(WHO)I级室管膜瘤,每年每10万人中发病0.05 - 0.08例。手术切除是推荐的一线治疗方法。由于该疾病罕见,对于放疗(RT)在治疗这种疾病中的应用了解相对较少。分析了国家癌症数据库(NCDB)中2002年至2016年诊断的成人MPE的治疗模式。在753例符合条件的病例中,大多数患者接受了手术切除(n = 617,81.9%)。接受RT的患者比例相对较小(n = 103,13.3%),其中大多数在术后接受RT(n = 98,95.1%)。患者接受手术切除和RT的可能性与诊断时的患者年龄(p = 0.002)、肿瘤大小(p < 0.001)和种族(p = 0.017)相关。化疗未得到广泛应用(占患者的0.27%)。我们分析的一个局限性是没有无进展生存期(PFS)的数据,鉴于该疾病的高生存率,PFS是一个重要的结果。手术仍然是治疗成人MPE的主要手段。对于脊髓MPE,据了解只要有可能应尝试进行全切除(GTR),因为在多项研究中GTR与改善的PFS相关。鉴于该队列中的死亡率为1.6%,RT对总生存期(OS)的影响尚不确定。在更大的数据库中分析RT对PFS的影响将有助于确定该疾病实体术后和确定性RT的算法。