Isıyel Emel, Bakkaloğlu Sevcan, Oğuz Deniz, Yenicesu İdil, Boyunağa Öznur, Özdemir Yeşim, Damar Çağrı, Kandur Yaşar, Akçaboy Meltem, Aslan Ayşe Tana, Şişmanlar Tuğba, Hasanoğlu Enver, Buyan Necla
Divisions of Pediatric Nephrology, Gazi University Faculty of Medicine, Ankara, Turkey.
Department of Pediatric Cardiology, Gazi University Faculty of Medicine, Ankara, Turkey.
Turk J Pediatr. 2019;61(4):585-588. doi: 10.24953/turkjped.2019.04.016.
Isıyel E, Bakkaloğlu S, Oğuz D, Yenicesu İ, Boyunağa Ö, Özdemir Y, Damar Ç, Kandur Y, Akçaboy M, Aslan AT, Şişmanlar T, Hasanoğlan E, Buyan N. An adolescent case of extensive Behçets disease successfully treated with Infliximab. Turk J Pediatr 2019; 61: 585-588. Cardiac involvement is an uncommon and life-threatening complication of Behçets Disease. We present a 14-year-old boy, admitted to our hospital for recurrent hemoptysis. In his radiologic evaluation, a right ventricular thrombus and pulmonary arterial aneurysm were identified. He was diagnosed with Behçets Disease, and then he received prednisone and cyclophosphamide. However, his cardiac thrombus enlargened. After his treatment was replaced with infliximab, the pulmonary aneurysms regressed, and the cardiac thrombus disappeared. In conclusion, infliximab should be considered as a reliable option for vascular Behçets Disease resistant to conventional treatment.
伊西尔·E、巴卡洛奥卢·S、奥乌兹·D、耶尼塞苏·İ、博尤纳加·Ö、厄兹德米尔·Y、达玛尔·Ç、坎杜尔·Y、阿克恰博伊·M、阿斯兰·A.T、希什曼拉尔·T、哈萨诺格兰·E、布扬·N。1例青少年广泛性白塞病经英夫利昔单抗成功治疗。《土耳其儿科学杂志》2019年；61:585 - 588。心脏受累是白塞病一种罕见且危及生命的并发症。我们报告1例14岁男孩，因反复咯血入住我院。在其影像学评估中，发现右心室血栓和肺动脉瘤。他被诊断为白塞病，随后接受了泼尼松和环磷酰胺治疗。然而，他的心脏血栓增大。在用英夫利昔单抗替代治疗后，肺动脉瘤消退，心脏血栓消失。总之，对于常规治疗耐药的血管性白塞病，英夫利昔单抗应被视为一种可靠的选择。
