Aladağ Çiftdemir Nükhet, Gökalp Selman, Eren Tuba
Department of Pediatrics, Trakya University Faculty of Medicine, Edirne, Turkey.
Department of Pediatrics, Cerrahpaşa University Faculty of Medicine, Istanbul, Turkey.
Arch Rheumatol. 2019 May 22;34(4):451-456. doi: 10.5606/ArchRheumatol.2019.7169. eCollection 2019 Dec.
Behçet's disease (BD) is a rare, multisystemic, chronic vasculitic disorder with unknown etiology. Intracardiac thrombus formation and pulmonary artery aneurysm in BD are very rare. The treatment protocol in patients with vascular involvement, particularly those with pulmonary artery aneurysm accompanied by thrombosis, have not been clearly defined. In this article, we report an exceptional case, who had been treated unsuccessfully with a combination of anti-inflammatory/immunosuppressive therapy and thrombolytic agents, to discuss the poor prognosis of pulmonary artery aneurysm accompanying intracardiac thrombosis in juvenile BD.
白塞病（BD）是一种病因不明的罕见的多系统慢性血管炎性疾病。白塞病中心腔内血栓形成和肺动脉瘤非常罕见。血管受累患者，尤其是伴有血栓形成的肺动脉瘤患者的治疗方案尚未明确界定。在本文中，我们报告了一例特殊病例，该病例接受抗炎/免疫抑制治疗和溶栓药物联合治疗未成功，以探讨青少年白塞病中心腔内血栓形成伴肺动脉瘤的不良预后。
