Alström 综合征患者的人工耳蜗植入和乳突填塞术。
Cochlear implantation and mastoid obliteration in a patient with Alström Syndrome.
机构信息
Mercer University School of Medicine. Macon, GA, United States.
Pediatric Ear, Nose, and Throat of Atlanta. Atlanta, GA, United States.
出版信息
Int J Pediatr Otorhinolaryngol. 2020 May;132:109894. doi: 10.1016/j.ijporl.2020.109894. Epub 2020 Jan 18.
OBJECTIVES
To describe the outcomes of cochlear implantation with mastoid obliteration in a patient with Alström Syndrome and chronic otorrhea.
METHODS
This is a single case discussion of a patient with Alström Syndrome and chronic otorrhea who underwent unilateral cochlear implantation and mastoid obliteration in January 2019. Subsequent contralateral procedure was performed 4 months later. Implantation was pursued due to the progressive sensorineural hearing-loss that is characteristic of Alström Syndrome. Serial Audiograms were obtained before and after procedure.
RESULTS
Following implantation, audiological reports improved to near normal thresholds from the previous 60-85 dB sloping hearing loss. The patient's language skills rapidly improved as well as the ability to express her personality. Mastoid obliteration effectively resolved the chronic otorrhea that further complicated this case.
CONCLUSION
Cochlear implantation with mastoid obliteration was successful in improving hearing thresholds and resolving chronic otorrhea in a patient with Alström Syndrome.
目的
描述 1 例 Alström 综合征伴慢性耳漏患者行乳突闭塞并人工耳蜗植入的结果。
方法
这是 1 例 Alström 综合征伴慢性耳漏患者的个案报道，该患者于 2019 年 1 月接受了单侧人工耳蜗植入和乳突闭塞术，4 个月后进行了对侧手术。由于 Alström 综合征的特征性进行性感觉神经性听力损失，因此进行了植入。在手术前后获得了系列听力图。
结果
植入后，听力报告从之前的 60-85dB 斜率听力损失改善至接近正常阈值。患者的语言技能迅速提高，表达个性的能力也提高了。乳突闭塞有效地解决了使该病例复杂化的慢性耳漏。
结论
在 Alström 综合征患者中，乳突闭塞并人工耳蜗植入术成功改善了听力阈值，并解决了慢性耳漏问题。
Zotero 插件