Postlethwaite K R, Parry D H
Department of Oral and Maxillofacial Surgery, Glan Clwyd Hospital, N. Wales.
Br J Oral Maxillofac Surg. 1988 Dec;26(6):499-502. doi: 10.1016/0266-4356(88)90072-1.
An unusual case of angioedema is presented. The initial presentation occurred at 84 years-of-age without a family history of this condition. Further investigation revealed an underlying lymphoproliferative disorder which was associated with an acquired deficiency of the complement component C1 esterase inhibitor. It is important to distinguish this condition from the hereditary form.
本文报告了一例罕见的血管性水肿病例。该病例首次发病于84岁,无该病家族史。进一步检查发现潜在的淋巴增殖性疾病,这与补体成分C1酯酶抑制剂的后天性缺乏有关。将这种情况与遗传性形式区分开来很重要。