Cui Yuanshan, Cui Yupeng, Zhang Yong
Department of Urology, Beijing Tian Tan Hospital, Capital Medical University, Beijing 100070, China.
Department of Urology, The Affiliated Yantai Yuhuangding Hospital of Qingdao University, Yantai 264000, China.
Transl Androl Urol. 2019 Dec;8(6):754-757. doi: 10.21037/tau.2019.12.02.
Renal ectopia occurs in 1:3,000-1:7,000 children. Simple ectopia refers to the abnormal kidney location on the same side; in crossed ectopia the ureter crosses the midline of the body. Pelvic ectopic solitary kidney with hydronephrosis due to ureteropelvic junction obstruction (UPJO) is even rarer in clinical practice. We report a case of a pelvic ectopic solitary kidney with hydronephrosis due to UPJO in an 18-year-old girl. Three-dimensional computed tomography (CT) scan showed the Single Ectopic Kidney with irregular shape lying in the pelvis and its cortex is very thin because of the grossly dilated renal pelvis and ureter. The terminal ureteral joined the right posterior wall of bladder. The renal artery originated from the bilateral common iliac artery, and laparoscopic pyeloplasty was performed. 18 months after the surgery, hydronephrosis was improved morphologically, and the estimated glomerular filtration rate was stable.
肾异位在儿童中的发生率为1:3000至1:7000。单纯异位是指肾脏在同侧的异常位置；交叉异位是指输尿管跨过身体中线。盆腔异位孤立肾伴因肾盂输尿管连接处梗阻（UPJO）导致的肾积水在临床实践中更为罕见。我们报告一例18岁女孩盆腔异位孤立肾伴因UPJO导致肾积水的病例。三维计算机断层扫描（CT）显示单个异位肾形状不规则，位于盆腔内，由于肾盂和输尿管明显扩张，其皮质非常薄。输尿管末端与膀胱右后壁相连。肾动脉起源于双侧髂总动脉，并进行了腹腔镜肾盂成形术。手术后18个月，肾积水在形态上得到改善，估计肾小球滤过率稳定。
