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先天性左心室憩室:心律失常的罕见病因。

Congenital left ventricular diverticulum: A rare cause of cardiac arrhythmia.

作者信息

Claus Isabelle, Adriaenssens Bert, Van Beeumen Katarina, Timmers Liesbeth, Bové Thierry

机构信息

Department of Cardiac Surgery, UZ Gent, Ghent, Belgium.

Department of Cardiology, AZ Nikolaas, Sint-Niklaas, Belgium.

出版信息

J Card Surg. 2020 Apr;35(4):926-929. doi: 10.1111/jocs.14464. Epub 2020 Feb 17.

DOI:10.1111/jocs.14464
PMID:32065468
Abstract

Congenital left ventricular diverticula are rare cardiac malformations that usually remain asymptomatic. However, life-threatening complications as ventricular arrhythmias, systemic embolism, spontaneous rupture and development of valvular regurgitation, are described. Diagnosis is based on excluding coronary artery disease, traumatic or inflammatory causes, and other underlying cardiomyopathies. Treatment is directed towards the potential complications, yielding mainly therapy of ventricular arrhythmia. Surgical resection is required for larger-sized congenital aneurysms with adverse hemodynamic effects. We present two cases of a left ventricular diverticulum causing cardiac arrhythmia which led to further surgical treatment.

摘要

先天性左心室憩室是一种罕见的心脏畸形,通常无症状。然而,也有危及生命的并发症的描述,如室性心律失常、系统性栓塞、自发性破裂和瓣膜反流的发展。诊断基于排除冠状动脉疾病、创伤性或炎症性病因以及其他潜在的心肌病。治疗针对潜在的并发症,主要是室性心律失常的治疗。对于具有不良血流动力学影响的较大先天性动脉瘤,需要进行手术切除。我们报告两例因左心室憩室导致心律失常并进而接受手术治疗的病例。

相似文献

1
Congenital left ventricular diverticulum: A rare cause of cardiac arrhythmia.先天性左心室憩室:心律失常的罕见病因。
J Card Surg. 2020 Apr;35(4):926-929. doi: 10.1111/jocs.14464. Epub 2020 Feb 17.
2
Congenital left ventricular diverticulum diagnosed by 64-detector CT imaging.64层螺旋CT成像诊断先天性左心室憩室
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[Congenital left ventricular aneurysms and diverticula. Pathophysiology, clinical relevance, and treatment].[先天性左心室动脉瘤和憩室。病理生理学、临床相关性及治疗]
Med Klin (Munich). 2007 May 15;102(5):358-65. doi: 10.1007/s00063-007-1034-3.
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Isolated congenital left ventricular diverticulum in adults.成人孤立性先天性左心室憩室
Indian Heart J. 2001 Mar-Apr;53(2):211-3.
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Congenital left ventricular diverticulum.
Heart Lung Circ. 2006 Aug;15(4):272-4. doi: 10.1016/j.hlc.2006.02.013. Epub 2006 Apr 19.
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[Congenital left ventricular aneurysms and diverticula. Two case reports].[先天性左心室动脉瘤和憩室。两例病例报告]
Ann Cardiol Angeiol (Paris). 1999 Jan;48(1):13-5.
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Congenital left ventricular diverticulum in a patient with coronary artery disease.先天性左心室憩室合并冠状动脉疾病患者。
J Chin Med Assoc. 2010 Aug;73(8):441-3. doi: 10.1016/S1726-4901(10)70095-2.
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[Congenital ventricular diverticulum associated with ventricular tachycardia].
Arq Bras Cardiol. 2005 Feb;84(2):173-5. doi: 10.1590/s0066-782x2005000200016. Epub 2005 Mar 8.
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Congenital left ventricular diverticula: a rare cause of sudden cardiac death.先天性左心室憩室:心脏性猝死的罕见原因。
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