Sinha Lok, Klein Katherine, Ramakrishnan Karthik, Jonas Richard
Department of Cardiovascular Surgery, Children's National Health System, Washington, DC, USA.
Department of Cardiothoracic Surgery, Virginia Commonwealth University, Richmond, VA, USA.
World J Pediatr Congenit Heart Surg. 2020 Mar;11(2):220-221. doi: 10.1177/2150135119888142.
Late systemic outflow tract obstruction following completion of the Fontan palliation is rarely seen and is a difficult problem to treat. Absence of the main pulmonary trunk and pulmonary valve at this stage makes a conventional Damus-Kaye-Stansel connection difficult to achieve. We report the case of a 37-year-old female who underwent Fontan completion as an adult and subsequently presented with systemic outflow tract obstruction. A valved conduit was interposed between the native pulmonary annulus and the ascending aorta to create a modified Damus-Kaye-Stansel type connection.
在Fontan姑息手术完成后出现的晚期体循环流出道梗阻很少见，且是一个难以治疗的问题。在此阶段，主肺动脉干和肺动脉瓣缺如使得传统的Damus-Kaye-Stansel连接难以实现。我们报告一例37岁成年女性患者，其成年后接受了Fontan完成手术，随后出现体循环流出道梗阻。在天然肺动脉瓣环与升主动脉之间置入一个带瓣管道，以建立改良的Damus-Kaye-Stansel型连接。
