Kotthoff S, Eigster G, Naib I, Vogt J
Abteilung Pädiatrische Kardiologie, Universitäts-Kinderklinik und Poliklinik, Göttingen.
Monatsschr Kinderheilkd. 1988 Jul;136(7):390-2.
A 3 week old neonate developed congestive heart failure after the operation of an omphalocele. The clinical aspect first suggested to us a persistent ductus arteriosus. Cardiac catheterisation then revealed a bronchopulmonary sequestration, a rare congenital malformation. Children usually become symptomatic with chronic respiratory tract infections, although there are also asymptomatic courses. Only a few cases are reported with congestive heart failure being the initial symptom. Many patients show additional malformations--so did our baby with an omphalocele and a mild peripheral pulmonary stenosis. Once the diagnosis is made, resection or lobectomy is the therapy of choice. In the preoperative diagnosis angiography is mandatory to demonstrate the abnormal vascular supply.
一名3周大的新生儿在脐膨出手术后出现充血性心力衰竭。临床症状最初让我们怀疑是动脉导管未闭。心脏导管检查随后发现是肺隔离症，这是一种罕见的先天性畸形。儿童通常会因慢性呼吸道感染出现症状，不过也有无症状的情况。仅有少数病例报告以充血性心力衰竭为首发症状。许多患者还伴有其他畸形，我们的婴儿就合并脐膨出和轻度外周肺动脉狭窄。一旦确诊，手术切除或肺叶切除术是首选治疗方法。术前诊断必须进行血管造影以显示异常的血管供应。
