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1例由遗传性肺动脉高压引起的奥尔特纳综合征儿科病例及文献复习

A pediatric case of Ortner`s syndrome caused by heritable pulmonary arterial hypertension and review of the literature.

作者信息

Kaya Özkan, Yoldaş Tamer, Karademir Selmin, Örün Utku Arman, Sarı Eyüp

机构信息

Division of Pediatric Cardiology, Dr. Sami Ulus Maternity, Children's Health and Diseases Training and Research Hospital, Ankara, Turkey.

Department of Pediatrics, Dr. Sami Ulus Maternity, Children's Health and Diseases Training and Research Hospital, Ankara, Turkey.

出版信息

Turk J Pediatr. 2019;61(6):963-966. doi: 10.24953/turkjped.2019.06.022.

DOI:10.24953/turkjped.2019.06.022
PMID:32134595
Abstract

Kaya Ö, Yoldaş T, Karademir S, Örün UA, Sarı E. A pediatric case of Ortners syndrome caused by heritable pulmonary arterial hypertension and review of the literature. Turk J Pediatr 2019; 61: 963-966. An 11-year-old male, who complained of hoarseness and fatigue on effort presented to our institution for evaluation. Left vocal cord paralysis and severe pulmonary hypertension was diagnosed. The patient had an enlarged pulmonary artery due to pulmonary hypertension which was responsible for compression to left vocal cord paralysis causing hoarseness. Ortners syndrome or cardiovocal syndrome is known as hoarseness due to left vocal cord paralysis secondary to cardiac pathologies. Although hoarseness of voice is frequently encountered in the otorhinolaryngology clinics, pulmonary hypertension related hoarseness is an unusual presentation in childhood.

摘要

卡亚·Ö、约尔达斯·T、卡拉德米尔·S、厄吕恩·UA、萨里·E。一例由遗传性肺动脉高压引起的奥尔特纳综合征儿科病例及文献综述。《土耳其儿科学杂志》2019年;61:963 - 966。一名11岁男性因主诉劳力时声音嘶哑和疲劳前来我院评估。诊断为左侧声带麻痹和重度肺动脉高压。该患者因肺动脉高压导致肺动脉增粗,压迫左侧声带引起麻痹,进而导致声音嘶哑。奥尔特纳综合征或心血管性发声综合征是指因心脏病变继发左侧声带麻痹而导致声音嘶哑。虽然声音嘶哑在耳鼻喉科门诊很常见,但与肺动脉高压相关的声音嘶哑在儿童中是一种不常见的表现。

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Ortner's Syndrome in an Infant With Congenital Heart Disease.一名患有先天性心脏病的婴儿的奥特纳综合征。
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