胸腔巨大恶性外周神经鞘瘤切除术。

Resection of a Huge Intrathoracic Malignant Peripheral Nerve Sheath Tumor.

机构信息

Department of Cardiothoracic Surgery, Faculty of Medical Science, Lebanese University, Beirut, Lebanon.

Department of Cardiothoracic Anesthesia, Lebanese Geitaoui University Hospital, Beirut, Lebanon.

出版信息

Ann Thorac Surg. 2020 Sep;110(3):e169-e171. doi: 10.1016/j.athoracsur.2020.01.046. Epub 2020 Mar 2.

DOI:10.1016/j.athoracsur.2020.01.046

PMID:32135151

Abstract

Malignant peripheral nerve sheath tumors, also known as malignant schwannoma, are rare soft tissue sarcomas. They commonly invade axial sites and rarely do they occur in the thorax. Herein, we present the case of an enormous metastatic multilobulated intrathoracic malignant peripheral nerve sheath tumor that was first misdiagnosed as desmoid fibromatosis and successfully resected for palliative purpose.

摘要

恶性外周神经鞘瘤，又称恶性神经鞘瘤，是一种罕见的软组织肉瘤。它们通常侵犯轴性部位，很少发生在胸部。在此，我们报告了 1 例巨大的转移性多叶性胸内恶性外周神经鞘瘤，最初误诊为硬纤维瘤病，为了缓解症状成功进行了切除。