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合并发育异常二叶式主动脉瓣的主动脉-左心室隧道的产前诊断:从胎儿心力衰竭到良好预后

Prenatal Diagnosis of Aorto-Left Ventricular Tunnel With Dysplastic Bicuspid Aortic Valve: From Fetal Cardiac Failure to Favorable Outcome.

作者信息

Truong Ba Luu, Moreau De Bellaing Anne, Vialle Emmanuelle, Haydar Ayman, Vouhe Pascal, Jouk Pierre Simon, Blaysat Gerard

机构信息

Pediatric Cardiac Unit, Hôpital Universitaire de Grenoble-Alpes, Grenoble, France.

Cardiovascular Unit, Children's Hospital 2, Ho Chi Minh City, Vietnam.

出版信息

Front Pediatr. 2020 Feb 27;8:69. doi: 10.3389/fped.2020.00069. eCollection 2020.

DOI:10.3389/fped.2020.00069
PMID:32175295
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC7056665/
Abstract

Aorto-left ventricular tunnel (ALVT) is a rare congenital heart defect. Surgery has to be performed early to avoid life-threatening complications. Prenatal diagnosis of this defect is challenging. We report a case of ALVT diagnosed in a fetus showing premature severe cardiac failure at 24 GA. The new born was operated at day 3 of life with good results. Two years later, he is still doing well recovering a complete normal cardiac function. ALVT should be suggested in front of any fetal cardiac failure. Thanks to early diagnosis, prompt neonatal management can be organized and allows positive outcome.

摘要

主动脉左心室隧道(ALVT)是一种罕见的先天性心脏缺陷。必须尽早进行手术以避免危及生命的并发症。这种缺陷的产前诊断具有挑战性。我们报告一例在孕24周时被诊断为ALVT的胎儿,该胎儿出现早产严重心力衰竭。新生儿在出生后第3天接受手术,效果良好。两年后,他恢复情况良好,心脏功能完全正常。面对任何胎儿心力衰竭都应考虑到ALVT。由于早期诊断,可以及时组织新生儿管理并取得良好结果。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/cf2d/7056665/60ab89018a5e/fped-08-00069-g0001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/cf2d/7056665/60ab89018a5e/fped-08-00069-g0001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/cf2d/7056665/60ab89018a5e/fped-08-00069-g0001.jpg

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本文引用的文献

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Aorto-Right Ventricular Tunnel in Transposition of the Great Arteries.大动脉转位中的主动脉-右心室通道
Front Pediatr. 2018 Feb 21;6:30. doi: 10.3389/fped.2018.00030. eCollection 2018.
2
Clinical implications of prenatal diagnosis of aorto-left ventricular tunnel on postnatal treatment and final outcome.主动脉左心室隧道产前诊断对产后治疗及最终结局的临床意义。
Turk J Pediatr. 2017;59(3):342-344. doi: 10.24953/turkjped.2017.03.019.
3
Congenital aortico-left ventricular tunnel in fetuses and infants.胎儿及婴儿先天性主动脉-左心室通道
J Med Ultrason (2001). 2013 Apr;40(2):153-6. doi: 10.1007/s10396-012-0414-3. Epub 2012 Nov 27.
4
Aorto-Left Ventricular Tunnel Successfully Repaired Immediately After Birth.主动脉-左心室隧道在出生后立即成功修复。
Ann Thorac Surg. 2016 May;101(5):1988-90. doi: 10.1016/j.athoracsur.2015.06.105.
5
Aortico-left ventricular tunnel and left ventricular non-compaction: a case series.主动脉-左心室通道与左心室心肌致密化不全:病例系列
Cardiol Young. 2016 Feb;26(2):382-5. doi: 10.1017/S1047951115001109. Epub 2015 Jun 22.
6
Prenatal diagnosis of aorto-left ventricular tunnel: introducing the 'cockade sign'.主动脉左心室隧道的产前诊断:介绍“帽徽征”
Eur Heart J. 2015 May 7;36(18):1136. doi: 10.1093/eurheartj/ehu525. Epub 2015 Feb 2.
7
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Echocardiography. 2014;31(1):E20-3. doi: 10.1111/echo.12396. Epub 2013 Oct 16.
8
Prenatal and pathologic features of aorto-left ventricular tunnel causing fetal hydrops and intrauterine demise.导致胎儿水肿和宫内死亡的主动脉-左心室通道的产前及病理特征
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Aortico-left ventricular tunnel: the elusive diagnosis.主动脉-左心室通道:难以捉摸的诊断
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