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调节剂治疗囊性纤维化患者：朝着正确的方向前进。

Modulator treatment for people with cystic fibrosis: moving in the right direction.

机构信息

Faculty of Medicine Health and Life Sciences, Queens University of Belfast, Belfast, UK

出版信息

Eur Respir Rev. 2020 Mar 20;29(155). doi: 10.1183/16000617.0051-2020. Print 2020 Mar 31.

DOI:10.1183/16000617.0051-2020
PMID:32198220
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC9489145/
Abstract

http://bit.ly/3akQ0tK

摘要

http://bit.ly/3akQ0tK

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Modulator treatment for people with cystic fibrosis: moving in the right direction.调节剂治疗囊性纤维化患者：朝着正确的方向前进。
Eur Respir Rev. 2020 Mar 20;29(155). doi: 10.1183/16000617.0051-2020. Print 2020 Mar 31.
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Ivacaftor for patients with cystic fibrosis.用于囊性纤维化患者的依伐卡托
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Novel, mechanism-based therapies for cystic fibrosis.针对囊性纤维化的新型、基于机制的疗法。
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Emerging technologies for cystic fibrosis transmembrane conductance regulator restoration in all people with CF.用于所有囊性纤维化跨膜电导调节因子（CFTR）患者 CFTR 修复的新兴技术。
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It's not all about inhaled treatment: challenges with oral therapy in paediatric respiratory medicine.并非全是吸入治疗：儿科呼吸医学中口服疗法面临的挑战。
Breathe (Sheff). 2021 Mar;17(1):210005. doi: 10.1183/20734735.0005-2021.

本文引用的文献

1
Impact of CFTR modulator use on outcomes in people with severe cystic fibrosis lung disease.CFTR 调节剂治疗对严重肺囊性纤维化患者结局的影响。
Eur Respir Rev. 2020 Mar 20;29(155). doi: 10.1183/16000617.0112-2019. Print 2020 Mar 31.
2
Adult Care in Cystic Fibrosis.囊性纤维化成人护理。
Semin Respir Crit Care Med. 2019 Dec;40(6):857-868. doi: 10.1055/s-0039-3400289. Epub 2019 Dec 30.
3
Lumacaftor/Ivacaftor reduces pulmonary exacerbations in patients irrespective of initial changes in FEV.无论初始 FEV 变化如何，Lumacaftor/Ivacaftor 均可减少患者的肺部恶化。
J Cyst Fibros. 2019 Jan;18(1):94-101. doi: 10.1016/j.jcf.2018.07.011. Epub 2018 Aug 23.
4
Cystic fibrosis.囊性纤维化。
Lancet. 2016 Nov 19;388(10059):2519-2531. doi: 10.1016/S0140-6736(16)00576-6. Epub 2016 Apr 29.