Zoubeidi H, Daoud F, Rachdi I, Somai M, Aydi Z, Ben Dhaou B, Boussema F
Service de médecine interne, hôpital Habib Thameur, 8, rue Ali Ben Ayed, 1008 Tunis, Tunisie; Faculté de médecine de Tunis, université de Tunis El Manar, Tunis, Tunisie.
Service de médecine interne, hôpital Habib Thameur, 8, rue Ali Ben Ayed, 1008 Tunis, Tunisie; Faculté de médecine de Tunis, université de Tunis El Manar, Tunis, Tunisie.
Ann Cardiol Angeiol (Paris). 2020 May;69(3):148-150. doi: 10.1016/j.ancard.2019.09.014. Epub 2020 Apr 4.
Churg-Strauss syndrome (CSS) or eosinophilic granulomatosis with polyangiitis is a systemic vasculitis characterized by necrotizing arteritis, eosinophilic infiltration and extravascular granuloma; that may involve several organs. Cardiac involvement is the first cause of death in this vasculitis. These include myocarditis, pericarditis, coronary heart disease, dysrhythmias, and rarely valvular involvement. We report the observation of CSS revealed by acute perimyocarditis.
变应性肉芽肿性血管炎(CSS)或嗜酸性肉芽肿性多血管炎是一种系统性血管炎,其特征为坏死性动脉炎、嗜酸性粒细胞浸润和血管外肉芽肿形成;可累及多个器官。心脏受累是这种血管炎的首要死因。这些表现包括心肌炎、心包炎、冠心病、心律失常,瓣膜受累则较为罕见。我们报告了一例以急性心肌心包炎为表现的CSS病例。