Division of Cardiovascular and Thoracic Surgery, Duke Children's Pediatric & Congenital Heart Center, Duke University Medical Center, Durham, North Carolina.
Division of Cardiovascular and Thoracic Surgery, Duke Children's Pediatric & Congenital Heart Center, Duke University Medical Center, Durham, North Carolina.
Ann Thorac Surg. 2020 Oct;110(4):e279-e280. doi: 10.1016/j.athoracsur.2020.03.038. Epub 2020 Apr 18.
Systemic right ventricle failure often develops in patients with dextro-transposition of the great arteries who have undergone atrial-level switch procedures. An adult with dextro-transposition of the great arteries with Mustard repair in childhood presented with end-stage heart failure due to systemic right ventricle failure, Mustard baffle leak, and unrepaired partial anomalous pulmonary venous return. She underwent device closure of the baffle leak by catheterization, followed by baffle revision and concomitant systemic ventricular assist device placement by adult and pediatric heart surgeons. This case demonstrates the importance of multidisciplinary collaboration between pediatric and adult heart failure specialists in caring for complex adult congenital heart patients.
系统性右心室衰竭在接受心房水平Switch 手术的右旋大动脉转位患者中常常会发生。一名曾行Mustard 修复术的儿童期右旋大动脉转位患者出现终末期心力衰竭,原因是系统性右心室衰竭、Mustard 隔瓣漏和未修复的部分肺静脉异常回流。她通过导管介入进行隔瓣漏封堵装置的闭合,随后由成人和儿科心脏外科医生进行隔瓣修复和同期系统心室辅助装置的植入。本病例展示了儿科和成人心力衰竭专家之间多学科合作在治疗复杂成人先天性心脏病患者中的重要性。