Madhala Divya, Sundaram Sandhya, Chinambedudandapani MohanaPriya, Balasubramanian Archana
Pathology, Sri Ramachandra Institute of Higher Education and Research, Chennai, IND.
Genetics, Sri Ramachandra Institute of Higher Education and Research, Chennai, IND.
Cureus. 2020 Mar 22;12(3):e7369. doi: 10.7759/cureus.7369.
Background Gastrointestinal stromal tumors (GIST) are the most common mesenchymal neoplasms in the gastrointestinal (GI) tract. The mutation of C-KIT is considered to be the crucial step in the tumorigenesis. Targeted therapies are being developed focusing these mutations. Various exon mutations of GIST responded in varied patterns to this targeted therapy. This study was carried out to evaluate the C-KIT exon 11, exon 9 and BRAF V600E mutations among GIST specimens. Methods This retrospective study was carried out among 20 DNA extracted specimens from paraffin blocks of GIST received in our tertiary teaching institution for a period of three years. DNA sequencing was carried out for mutational analyses on C-KIT exon 9, C-KIT exon 11 and BRAF V600E genes using Sanger sequencing. Results Histologically, majority of the tumors had spindle cell morphology. About 19 cases were positive for CD117. The analysis of type of mutations showed that three cases carried Exon 11 and three cases carried Exon 9 mutations. BRAF V600E mutation was seen in one case. Conclusion It is essential to conduct molecular studies on GISTs in order to get a clear understanding of the pathogenesis and behavior pattern. This will also help in designing targeted therapies and assessing recurrence. With the advent of rapidly evolving personalized therapy, the evaluation of genetic mutations is essential for diagnosis and prognostic value.
背景 胃肠道间质瘤(GIST)是胃肠道最常见的间叶性肿瘤。C-KIT突变被认为是肿瘤发生的关键步骤。针对这些突变正在开发靶向治疗。GIST的各种外显子突变对这种靶向治疗有不同的反应模式。本研究旨在评估GIST标本中C-KIT外显子11、外显子9和BRAF V600E突变情况。方法 本回顾性研究对我们三级教学机构在三年期间接收的20例从GIST石蜡块中提取的DNA标本进行。使用桑格测序法对C-KIT外显子9、C-KIT外显子11和BRAF V600E基因进行突变分析的DNA测序。结果 组织学上,大多数肿瘤具有梭形细胞形态。约19例CD117呈阳性。突变类型分析显示,3例携带外显子11突变,3例携带外显子9突变。1例出现BRAF V600E突变。结论 对GIST进行分子研究对于清楚了解其发病机制和行为模式至关重要。这也将有助于设计靶向治疗和评估复发情况。随着快速发展的个性化治疗的出现,基因突变评估对于诊断和预后价值至关重要。