Klochkov S A, Potapova I N, Potapova-Vinogradova I N
Arkh Patol. 1988;50(11):60-6.
Pathomorphology of congenital liver fibrosis (CLF) was studied basing on histological evaluation of 42 primary and secondary liver biopsies obtained from 26 CLF children aged 1-13. CLF age-specific complications, their variants and incidence rate as well as morphogenesis are outlined, e. g. cholangiolitis and secondary cirrhosis which are not rare in 7-13-year-old children. Presented is CLF staging.
基于对26名年龄在1至13岁的先天性肝纤维化（CLF）患儿的42份原发性和继发性肝活检组织进行组织学评估，对先天性肝纤维化的病理形态学进行了研究。概述了CLF的特定年龄并发症、其变体、发病率以及形态发生，例如在7至13岁儿童中并不罕见的胆管炎和继发性肝硬化。介绍了CLF的分期。
