Epilepsy Center, Neurological Institute, Cleveland Clinic , Cleveland, Ohio.
Neurodiagn J. 2020 Jun;60(2):113-127. doi: 10.1080/21646821.2020.1750879. Epub 2020 May 5.
Epilepsy with eyelid myoclonia or Jeavons Syndrome is a unique idiopathic generalized epilepsy with onset in childhood. It is characterized by eyelid myoclonia which may be associated with absence seizures, eyelid closure-induced epileptiform discharges and/or seizures and photosensitivity. It is frequently underrecognized and misdiagnosed because it may be mistaken for some other type of generalized epilepsy or facial tic disorder. The intent of this narrative review is to focus on existing literature and highlight the distinct electroencephalographic features including characteristic eye movements, associated waveforms, interictal and ictal findings that are suggestive and characteristic of Jeavons Syndrome to aid in timely recognition of this syndrome.
眼睑肌阵挛性癫痫或杰文斯综合征是一种独特的特发性全面性癫痫，发病于儿童期。其特征为眼睑肌阵挛，可能伴有失神发作、眼睑闭合诱发的癫痫样放电和/或癫痫发作以及光敏性。由于它可能被误诊为其他类型的全面性癫痫或面肌抽搐障碍，因此经常被低估和误诊。本综述的目的是重点关注现有文献，并强调具有特征性的脑电图特征，包括特征性的眼球运动、相关波形、发作间期和发作期发现，这些都提示和具有杰文斯综合征的特征，有助于及时识别这种综合征。
