Discipline of Surgery, The University of Sydney, Sydney, New South Wales, Australia
Department of Otolaryngology, Head & Neck Surgery, Gosford Hospital, Gosford, New South Wales, Australia.
BMJ Case Rep. 2020 May 4;13(5):e233345. doi: 10.1136/bcr-2019-233345.
Acquired haemophilia A is a rare but important diagnosis, carrying a mortality rate of 22%. Life-threatening sequalae of this diagnosis includes airway compromise, which can rapidly lead to demise of the patient if left untreated. Our case examines an 80-year-old man presenting with a supraglottic haematoma resulting from acquired haemophilia A causing airway compromise and necessitating definitive airway control. A review of current understanding and management of the disease is also ddiscussed.
获得性血友病 A 是一种罕见但重要的诊断,死亡率为 22%。该诊断的危及生命的后果包括气道阻塞,如果不治疗,可迅速导致患者死亡。我们的病例检查了一名 80 岁男性,因获得性血友病 A 导致声门上血肿导致气道阻塞,并需要明确的气道控制。还讨论了对该疾病的当前理解和管理的回顾。