Thangasami Senthilraj, Sahoo Sibasis Shasikant, Chandrasekaran Ananthanarayanan, Raval Pratik, Shaniswara Parth
Department of Cardiology, Un Mehta Institute of Cardiology and Research Institute, Asarwa, Ahmedabad, India.
Department of Cardiothoracic Surgery, Un Mehta Institute of Cardiology and Research Institute, Asarwa, Ahmedabad, India.
J Cardiol Cases. 2020 Mar 11;21(5):193-196. doi: 10.1016/j.jccase.2020.02.008. eCollection 2020 May.
Sub-mitral aneurysm (SMA) is a rare cardiac malformation commonly reported in young adults of African ancestry. SMA is considered a congenital disease caused by developmental defect due to weakness at the atrioventricular junction near the posterior mitral annulus. In the past two decades, a considerable number of cases regarding this rare disease have been reported in Asians, highlighting the importance of considering SMA in differential diagnosis of young patients presenting with mitral regurgitation and chest pain. Herein, we report the case of a young male with atypical chest pain with compression of left circumflex coronary artery by a large SMA. < Sub-mitral aneurysm is a rare cardiac malformation, caused by developmental defect due to weakness at the atrioventricular junction near the posterior mitral annulus. Patients may be entirely asymptomatic, or they can present with mitral regurgitation with or without left ventricular dysfunction, heart failure, systemic thromboembolism, ventricular wall rupture causing tamponade, myocardial ischemia due to compression of coronary arteries, ventricular arrhythmias, or sometimes sudden cardiac death. Strong suspicion and early diagnosis followed by surgery can prevent sudden cardiac death.>.
二尖瓣下动脉瘤(SMA)是一种罕见的心脏畸形,常见于非洲裔年轻成年人。SMA被认为是一种先天性疾病,由二尖瓣后瓣环附近房室交界处的薄弱导致发育缺陷引起。在过去二十年中,亚洲人中有相当数量关于这种罕见疾病的病例报道,这凸显了在鉴别诊断出现二尖瓣反流和胸痛的年轻患者时考虑SMA的重要性。在此,我们报告一例年轻男性病例,其因巨大的SMA压迫左旋支冠状动脉而出现非典型胸痛。<二尖瓣下动脉瘤是一种罕见的心脏畸形,由二尖瓣后瓣环附近房室交界处的薄弱导致发育缺陷引起。患者可能完全无症状,也可能表现为伴有或不伴有左心室功能障碍的二尖瓣反流、心力衰竭、全身性血栓栓塞、心室壁破裂导致心包填塞、冠状动脉受压引起的心肌缺血、室性心律失常,或有时发生心源性猝死。高度怀疑并早期诊断后进行手术可预防心源性猝死。>