[Case of Jakob-Creutzfeldt disease with rarely observed location of lesions (the so-called Heidenhain syndrome)].

The authors describe a case of Jakob-Creutzfeldt disease in a 64-year-old women. The peculiarity of the case lay in the fact that besides atrophic lesions of frontal lobes, extensive spongiform degeneration was present in both occipital lobes--corresponding to the so-called Heidenhain syndrome of classical neuropathology. The clinical counterpart of this location of the lesions, apart from dementia, were quadrantic hemianopsia and changes in EEG records.