Division of Pediatric Neurosurgery, Seoul National University Children's Hospital, Seoul National University College of Medicine, Seoul, South Korea.
Department of Anatomy and Cell Biology, Seoul National University College of Medicine, Seoul, South Korea.
Childs Nerv Syst. 2021 Jan;37(1):277-286. doi: 10.1007/s00381-020-04650-2. Epub 2020 May 12.
Nonsyndromic, multi-suture craniosynostosis is not common, especially those involving unilateral coronal and lambdoid sutures. Based on the experience on 6 cases, we analyzed the skull morphology of combined unilateral coronal-lambdoid suture synostosis and evaluated the surgical outcome of suturectomy.
Patients who underwent an operation for craniosynostosis in Seoul National University Children's Hospital from 2010 to 2018 were reviewed. For qualitative analysis of the surgical outcome, five typical morphologic characteristics (ipsilateral superior orbital rim deviation, deviation of the nasal ridge, ipsilateral frontal flattening, contralateral parietal bulging, ipsilateral occipitomastoid bulging) in unilateral coronal-lambdoid suture synostosis were evaluated based on medical photos, plain skull radiographs, and CT scans. For quantitative analysis, three parameters (nasal root deviation, orbital asymmetry, posterior skull base deviation) were measured.
Among 316 patients with craniosynostosis, 41 patients had nonsyndromic, multi-suture synostosis. There were 6 unilateral coronal-lambdoid suture synostosis patients who were all treated with suturectomy. Qualitative evaluation of the postoperative outcome revealed that the nasal root and orbital rim deviations and the contralateral occipitomastoid bulging showed satisfactory improvements. However, ipsilateral frontal flattening and contralateral parietal bulging were improved but still present in most cases. Quantitative, craniometric analysis supported the qualitative outcomes. The nasal ridge deviation angle was corrected from 7.04 to 1.79 degrees. The posterior skull base deviation angle improved from 6.29 to 3.55 degrees.
Unilateral coronal-lambdoid suture synostosis suturectomy followed by helmet therapy resulted in favorable outcomes, although the correction of frontal flattening was less satisfactory than the other measures. Considering the minimal invasiveness of the treatment, suturectomy may be a viable option for these patients.
非综合征性多缝颅缝早闭并不常见,尤其是涉及单侧冠状缝和人字缝的情况。基于 6 例病例的经验,我们分析了单侧冠状缝-人字缝联合性颅缝早闭的颅骨形态,并评估了颅缝切除术的手术效果。
回顾了 2010 年至 2018 年在首尔国立大学儿童医院接受颅缝早闭手术的患者。为了定性分析手术效果,根据影像学资料(包括头颅正侧位片和 CT 扫描),评估单侧冠状缝-人字缝早闭的 5 种典型形态特征(同侧眶上缘偏斜、鼻梁偏斜、同侧额骨扁平、对侧顶骨膨隆、同侧枕乳突部膨隆)。为了定量分析,测量了 3 个参数(鼻根偏斜、眼眶不对称、颅底后份偏斜)。
在 316 例颅缝早闭患者中,41 例为非综合征性多缝颅缝早闭,其中 6 例为单侧冠状缝-人字缝早闭,均行颅缝切除术。术后结果的定性评估显示,鼻根和眶缘偏斜以及对侧枕乳突部膨隆得到了明显改善。然而,同侧额骨扁平以及对侧顶骨膨隆虽有所改善,但在大多数病例中仍存在。颅测量分析支持定性结果,鼻嵴偏斜角度从 7.04°矫正至 1.79°,颅底后份偏斜角度从 6.29°改善至 3.55°。
单侧冠状缝-人字缝早闭行颅缝切除术联合头盔治疗可获得良好的效果,尽管额骨扁平的矫正效果不如其他指标满意。考虑到治疗的微创性,颅缝切除术可能是这些患者的可行选择。