Mohammadi Oranus, Suarez Manuel
Aventura Hospital and Medical Center
Westchester General Hospital
Glomangiomas, or glomuvenous malformations (GVM), are rare cutaneous venous malformations that show glomus cells (undifferentiated smooth muscle cells, which are thermoregulatory units), along with the venous system in histology. Glomus cells are specialized smooth muscle cells that regulate the temperature in the body. Masson first described glomangiomas, and Papoff further extensively studied them. There are 3 types of glomus tumors, classified based on their dominant component: : 1. Solid: mainly glomus cells. 2. Glomangioma: mainly blood vessels. 3. Glomangiomyoma: mainly smooth muscle cells : Glomangiomas are further divided into regional, disseminated, and congenital plaque-like. . Glomangiomas usually present in multiples, often at birth or during childhood, and they do not involve the subungual region. A majority of glomangiomas are benign, although malignant cases have also been reported. Rarely seen, the disseminated type distributes throughout the body.
血管球瘤,即静脉血管畸形(GVM),是一种罕见的皮肤静脉畸形,在组织学上表现为血管球细胞(未分化的平滑肌细胞,是体温调节单位)以及静脉系统。血管球细胞是调节体温的特殊平滑肌细胞。马森首次描述了血管球瘤,帕波夫进一步对其进行了广泛研究。血管球瘤有3种类型,根据其主要成分分类:1. 实体型:主要为血管球细胞。2. 血管瘤型:主要为血管。3. 血管球肌瘤型:主要为平滑肌细胞。血管球瘤进一步分为局限性、播散性和先天性斑块状。血管球瘤通常为多发,常在出生时或儿童期出现,不累及甲下区域。大多数血管球瘤是良性的,尽管也有恶性病例的报道。播散型很少见,可分布于全身。