Siraj M M, Khondokar N N, Alam K, Talukder A, Khanal A, Habib S A, Shakil S S, Rahman F
Dr Mohamed Mausool Siraj, MD Cardiology Phase B Student, University Cardiac Centre, Bangabandhu Sheikh Mujib Medical University (BSMMU), Dhaka, Bangladesh; E-mail:
Mymensingh Med J. 2020 Apr;29(2):464-468.
Dextrocardia with situs inversus is a state which is characterized by abnormal positioning of the heart and other internal organs. It is a rare congenital anomaly and the exact cause is not known. More than 60 recognized genes are significant for the proper positioning and patterning of the organs in the body. However, a specific genetic cause of dextrocardia with situs inversus has not been identified and inheritance prototypes have not been established in the majority cases. There are partial available case reports of successful percutaneous coronary intervention (PCI) in these patients who have atherosclerotic coronary artery disease, especially when presenting with myocardial infarction. PCI is technically difficult because of dextrocardia. We hereby describe a 51-year-old male, who had a recent inferior wall myocardial infarction and underwent successful coronary angiography and PCI at a tertiary level hospital in Dhaka, Bangladesh.
右位心伴内脏转位是一种以心脏和其他内脏器官位置异常为特征的状态。它是一种罕见的先天性异常,确切病因尚不清楚。超过60种已识别的基因对身体器官的正确定位和形态形成具有重要意义。然而,右位心伴内脏转位的具体遗传原因尚未确定,大多数情况下也未建立遗传模式。对于患有动脉粥样硬化性冠状动脉疾病的这些患者,尤其是出现心肌梗死时,有部分成功进行经皮冠状动脉介入治疗(PCI)的病例报告。由于右位心,PCI在技术上具有挑战性。我们在此描述一名51岁男性,他近期发生下壁心肌梗死,并在孟加拉国达卡的一家三级医院成功进行了冠状动脉造影和PCI。