Hotta Viviane Tiemi, Giorgi Maria Clementina Pinto, Fernandes Fábio, Abduch Maria Cristina Donadio, Falcão Andréa Maria Gomes Marinho, Mady Charles
. Instituto do Coração (InCor), Hospital das Clínicas HCFMUSP, Faculdade de Medicina, Universidade de São Paulo, São Paulo, SP, Brasil.
. Fleury Medicina e Saúde, São Paulo, SP, Brasil.
Rev Assoc Med Bras (1992). 2020 Mar;66(3):345-352. doi: 10.1590/1806-9282.66.3.345.
Cardiac amyloidosis is an infiltrative disease which requires a high degree of clinical suspicion for appropriate diagnosis. Early diagnosis and the definition of the type of amyloidosis play a key role in the early treatment and prognosis of this disease. In this context, the use of cardiac biomarkers such as troponins and NT-proBNT associated with analysis by multimodality imaging methods like echocardiographic techniques such as strain, nuclear medicine, and cardiovascular resonance imaging have an increasing role in patients with cardiac amyloidosis. This article details the role of non-invasive diagnostic methods in patients with cardiac amyloidosis.
心脏淀粉样变性是一种浸润性疾病,需要高度的临床怀疑才能做出准确诊断。淀粉样变性类型的早期诊断和明确在该疾病的早期治疗和预后中起着关键作用。在这种情况下,使用心肌生物标志物如肌钙蛋白和NT-proBNT,结合多模态成像方法进行分析,如应变超声心动图技术、核医学和心血管磁共振成像,在心脏淀粉样变性患者中发挥着越来越重要的作用。本文详细阐述了非侵入性诊断方法在心脏淀粉样变性患者中的作用。