Department of Otolaryngology, Massachusetts Eye and Ear Infirmary, Boston, Massachusetts, U.S.A.
Department of Pathology, Massachusetts Eye and Ear Infirmary, Boston, Massachusetts, U.S.A.
Laryngoscope. 2021 Mar;131(3):656-659. doi: 10.1002/lary.28848. Epub 2020 Jun 20.
Systemic disease is an uncommon cause of subglottic stenosis (SGS). We report a case of severe SGS due to underlying eosinophilic granulomatosis with polyangiitis (EGPA) in a child presenting with isolated stridor. EGPA is a rare systemic vasculitis with very limited cases reported in the pediatric population. While surgical intervention was required given the degree of stenosis in this case, medical management of the underlying systemic disease process is critical when there is clinical suspicion of SGS in the context of systemic vasculitis. Laryngoscope, 131:656-659, 2021.
系统性疾病是声门下狭窄（SGS）的不常见病因。我们报告了一例儿童因嗜酸性肉芽肿伴多血管炎（EGPA）引起的严重 SGS 病例，该患儿以孤立性喘鸣为主要表现。EGPA 是一种罕见的系统性血管炎，在儿科人群中报告的病例非常有限。鉴于该病例的狭窄程度，需要进行手术干预，但在系统性血管炎的背景下出现 SGS 的临床怀疑时，对潜在系统性疾病过程的药物治疗至关重要。《喉镜》，131：656-659，2021.
