Mayer Steffi, Gitter Heidrun, Göbel Peter, Hirsch Franz Wolfgang, Höhne Claudia, Hosie Stuart, Hubertus Jochen, Leutner Andreas, Muensterer Oliver, Schmittenbecher Peter, Seidl Elias, Stepan Holger, Thome Ulrich, Till Holger, Widenmann-Grolig Anke, Lacher Martin
Department of Pediatric Surgery, University Hospital Leipzig, Leipzig.
Department of Pediatric Surgery and Urology, Klinikum Bremen-Mitte, Children's Hospital, Bremen.
Klin Padiatr. 2020 Jul;232(4):178-186. doi: 10.1055/a-1149-9483. Epub 2020 Jun 26.
Esophageal atresia (EA) is a congenital anomaly that entails an interrupted esophagus with or without tracheoesophageal fistula (TEF). Depending on the distance of the two esophageal pouches a "short-gap" is distinguished from a "long-gap" variant. Up to 50% of newborns have additional anomalies. EA is prenatally diagnosed in 32-63% of cases. Recently, the interdisciplinary care in these children underwent substantial changes. Therefore, we summarize the current guideline of the German society of pediatric surgery for the treatment of patients with EA and distal TEF (Gross Type C). Controversies regarding the perioperative management include surgical-technical aspects, such as the thoracoscopic approach to EA, as well as general anesthesia (preoperative tracheobronchoscopy, intraoperative hypercapnia and acidosis). Moreover, postoperative complications and their management like anastomotic stricture are outlined. Despite significant improvements in the treatment of EA, there is still a relevant amount of long-term morbidity after surgical correction. This includes dysmotility of the esophagus, gastroesophageal reflux disease, recurrent respiratory infections, tracheomalacia, failure to thrive, and orthopedic complications following thoracotomy in the neonatal age. Therefore, close follow-up is mandatory to attain optimal quality of life.
食管闭锁(EA)是一种先天性异常,表现为食管中断,可伴有或不伴有气管食管瘘(TEF)。根据两个食管盲端的距离,可将“短间隙”型与“长间隙”型区分开来。高达50%的新生儿伴有其他异常。32% - 63%的病例在产前被诊断出EA。最近,对这些患儿的多学科护理发生了重大变化。因此,我们总结了德国小儿外科学会关于治疗EA合并远端TEF(C型总类)患者的现行指南。围手术期管理方面的争议包括手术技术方面,如EA的胸腔镜手术方法,以及全身麻醉(术前气管支气管镜检查、术中高碳酸血症和酸中毒)。此外,还概述了术后并发症及其处理,如吻合口狭窄。尽管EA的治疗有了显著改善,但手术矫正后仍有相当数量的长期发病率。这包括食管动力障碍、胃食管反流病、反复呼吸道感染、气管软化、生长发育不良以及新生儿期开胸术后的骨科并发症。因此,必须进行密切随访以获得最佳生活质量。