新生儿咽腔外脑脊膜脉络丛乳头状瘤伴气道梗阻：1 例报告。
Extracerebral choroid plexus papilloma in the pharynx with airway obstruction in a newborn: a case report.
机构信息
Department of Pediatrics, Pusan National University School of Medicine, 20 Geumo-ro, Yangsan, 50612, Republic of Korea.
Department of Radiology, Pusan National University School of Medicine, Yangsan, Republic of Korea.
出版信息
BMC Pediatr. 2020 Jul 7;20(1):336. doi: 10.1186/s12887-020-02234-2.
BACKGROUND
Choroid plexus papillomas (CPPs) are rare, usually benign, neoplasms originating in the central nervous system. In this study, we present the first case of a giant airway-obstructing CPP in the pharynx of a newborn.
CASE PRESENTATION
A cystic mass located in the pharynx was noted in a fetus at the 29th week of gestation. Elective cesarean section was performed at the 38th week of gestation with successful intubation and ex utero intrapartum treatment. On computed tomography, there was a huge airway-obstructing cystic mass in the choana and pharynx. Elective surgery with total excision was performed, and histological examination confirmed the diagnosis of CPP.
CONCLUSION
We report the first case of an extracerebral airway-obstructing CPP in the pharynx of a newborn. Radiologic examinations are not enough for the diagnosis of CPPs, and complete excision of the tumor with histological confirmation is indispensable for accurate diagnosis and treatment.
背景
脉络丛乳头状瘤（CPPs）是起源于中枢神经系统的罕见良性肿瘤。本研究报告首例发生于新生儿咽部的巨大气道阻塞性 CPP。
病例介绍
在妊娠 29 周的胎儿中发现咽部有一个囊性肿块。妊娠 38 周时行选择性剖宫产术，成功进行了插管和子宫外产时治疗。在计算机断层扫描（CT）上，后鼻孔和咽部有一个巨大的气道阻塞性囊性肿块。行择期完全切除术，组织学检查证实为 CPP。
结论
我们报告首例发生于新生儿咽部的脑外气道阻塞性 CPP。影像学检查对于 CPP 的诊断并不足够，完整切除肿瘤并进行组织学确认对于准确诊断和治疗是必不可少的。
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