Department of Radiology, Wake Forest Health, Winston-Salem, NC.
Department of Cardiothoracic Surgery, Wake Forest Health, Winston-Salem, NC.
J Vasc Surg Venous Lymphat Disord. 2020 Sep;8(5):864-868. doi: 10.1016/j.jvsv.2020.03.013. Epub 2020 Jul 9.
An 11-year-old girl with kaposiform lymphangiomatosis presented with recurrent chylous pericardial effusions that were refractory to pericardial drainage and medical therapy. Magnetic resonance imaging demonstrated a prominent lymphatic duct with anterior mediastinal extension into the left clavicular region and a region of high signal that was favored to represent a low-flow lymphatic malformation. The patient underwent direct access thoracic duct lymphangiography with thoracic duct embolization and sclerotherapy of the large left-sided neck and pericardial lymphatic malformation. After the procedure, her pericardial effusions resolved, and she has remained asymptomatic for 15 months.
一位 11 岁的女孩患有卡波西样淋巴管瘤病，表现为反复发作的乳糜性心包积液，对心包引流和药物治疗均有抗性。磁共振成像显示，一条明显的淋巴管向前纵隔延伸至左锁骨区域，存在一个高信号区域，该区域很可能代表低流量淋巴管畸形。患者接受了直接入路胸导管淋巴管造影术，对胸导管进行了栓塞，并对左侧颈部和心包大淋巴管畸形进行了硬化治疗。该操作后，患者心包积液消退，15 个月来一直无症状。
