Morley T F, Silverstein S D, Giudice J C, Csere R S
Department of Internal Medicine, University of Medicine and Dentistry of New Jersey, School of Osteopathic Medicine, Stratford.
Respiration. 1988;54(2):89-93. doi: 10.1159/000195506.
A 22-year-old black male presented with progressive dyspnea, a nonproductive cough, and new skin lesions. He was severely hypoxic, and had a severe restrictive defect on pulmonary function testing. A 2-cm lytic defect was noted on skull radiographs. A lung biopsy demonstrated pulmonary fibrosis. A biopsy of a skin lesion was consistent with a diagnosis of multifocal eosinophilic granuloma, or disseminated histiocytosis X. The case presents several unusual features of this uncommon disorder.
一名22岁的黑人男性出现进行性呼吸困难、干咳和新的皮肤病变。他严重缺氧，肺功能测试显示有严重的限制性缺陷。颅骨X线片显示有一个2厘米的溶骨性缺损。肺活检显示有肺纤维化。皮肤病变活检结果符合多灶性嗜酸性肉芽肿或播散性组织细胞增多症X的诊断。该病例呈现了这种罕见疾病的几个不寻常特征。
