Miyawaki Edison K, Hsu Liangge, Bhattacharyya Shamik, O'Hare Meabh J, Roy Alexis, Kett Lauren, Caplan Rachel A, Dattilo Lillian W, Jo Vickie Y, Guenette Jeffrey P
Department of Neurology, Brigham and Women's Hospital, Harvard Medical School, Boston, Massachusetts, USA.
Division of Neuroradiology, Brigham and Women's Hospital, Dana-Farber Cancer Institute, Harvard Medical School, Boston, Massachusetts, USA.
Case Rep Neurol. 2020 Jul 1;12(2):247-254. doi: 10.1159/000507920. eCollection 2020 May-Aug.
We report two cases of biopsy-corroborated "fibrosing inflammatory pseudotumor" to illustrate that the entity, rarely described in the neurological literature, should be included in the differential diagnosis of either a cranial mononeuropathy or, certainly, in the case of progressive cranial neuropathies. A broad differential diagnosis arises in certain contexts. Early steroid treatment can be effective, and perhaps later-generation immune-modulating agents may confer further options, although there is no known definitive treatment.
