脊髓发育不良患儿的管理

The management of children with spinal dysraphism.

作者信息

Liptak G S, Bloss J W, Briskin H, Campbell J E, Hebert E B, Revell G M

机构信息

Department of Pediatrics, University of Rochester School of Medicine and Dentistry, NY 14642.

出版信息

J Child Neurol. 1988 Jan;3(1):3-20. doi: 10.1177/088307388800300102.

DOI:10.1177/088307388800300102

PMID:3278049

Abstract

Improvements in technology have dramatically increased the survival of children with spinal dysraphism. Because this complex condition affects multiple organ systems as well as the psychosocial functioning of the child and family, these children require care from a host of specialists in order to achieve optimum functioning. This article reviews the pathophysiology and discusses the current management of the medical and psychosocial effects of spinal dysraphism. It also briefly discusses strategies for intervention, long-term outcomes, and some controversies regarding care and screening.

摘要

技术的进步显著提高了脊柱裂患儿的存活率。由于这种复杂病症会影响多个器官系统以及患儿及其家庭的心理社会功能，这些患儿需要众多专家的护理，以实现最佳功能状态。本文回顾了病理生理学，并讨论了目前对脊柱裂的医学和心理社会影响的管理。它还简要讨论了干预策略、长期结果以及一些关于护理和筛查的争议。