采用带蒂血管化腓骨移植保留部分皮质的节段间切除术治疗骨纤维结构不良样造釉细胞瘤：1例报告
Osteofibrous dysplasia-like adamantinoma treated via intercalary segmental resection with partial cortex preservation using pedicled vascularized fibula graft: a case report.
作者信息
Yamamura Yuji, Emori Makoto, Takahashi Nobuyuki, Chiba Mitsumasa, Shimizu Junya, Murahashi Yasutaka, Sugita Shintaro, Iba Kousuke, Hasegawa Tadashi, Yamashita Toshihiko
机构信息
Department of Orthopedic Surgery, Sapporo Medical University School of Medicine, West 16, South 1, Chuo- ku, Sapporo, Hokkaido, 060-8543, Japan.
Department of Diagnostic Pathology, Sapporo Medical University School of Medicine, Sapporo, Hokkaido, Japan.
出版信息
World J Surg Oncol. 2020 Aug 13;18(1):203. doi: 10.1186/s12957-020-01983-9.
BACKGROUND
Morphologically, osteofibrous dysplasia-like adamantinoma is thought to be intermediate between osteofibrous dysplasia and adamantinoma. Its treatment is not well established owing to its rarity.
CASE PRESENTATION
We report about of a 10-year-old girl with osteofibrous dysplasia-like adamantinoma initially diagnosed as osteofibrous dysplasia and treated via intercalary segmental resection with partial cortex preservation using a pedicled vascularized fibula graft for reconstruction. Bone union was observed 9 weeks after surgery. Twenty-two months after the definitive surgery, no recurrence was observed.
CONCLUSION
This case illustrates the upgrade from osteofibrous dysplasia to osteofibrous dysplasia-like adamantinoma. The surgical method may aid the treatment of osteofibrous dysplasia-like adamantinoma with incomplete cortex involvement of the tumor.
背景
从形态学上看，骨纤维异常增殖症样造釉细胞瘤被认为介于骨纤维异常增殖症和造釉细胞瘤之间。由于其罕见性，其治疗方法尚未完全确立。
病例报告
我们报告了一名10岁女孩，患有骨纤维异常增殖症样造釉细胞瘤，最初被诊断为骨纤维异常增殖症，并通过节段间切除并保留部分皮质，采用带蒂血管化腓骨移植进行重建治疗。术后9周观察到骨愈合。确定性手术后22个月，未观察到复发。
结论
本病例说明了从骨纤维异常增殖症到骨纤维异常增殖症样造釉细胞瘤的病情进展。该手术方法可能有助于治疗肿瘤皮质受累不完全的骨纤维异常增殖症样造釉细胞瘤。
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