Hedgpeth M T, Boulware D W
Section of Rheumatology, Tulane University Medical Center, New Orleans, LA 70112.
Ann Rheum Dis. 1988 Mar;47(3):251-3. doi: 10.1136/ard.47.3.251.
The clinical course of a patient with pulmonary hypertension associated with Sjögren's syndrome is reported. The clinical features and outcome of this case are compared with those of two other reported cases in the Spanish and Japanese published work. Thus far, pulmonary hypertension has not been reported with primary Sjögren's syndrome in English publications. These three cases suggest that the development of pulmonary hypertension in primary Sjögren's syndrome is uncommon but should be included as part of the clinical spectrum.
本文报告了一例与干燥综合征相关的肺动脉高压患者的临床病程。将该病例的临床特征及转归与西班牙和日本已发表文献中报道的另外两例病例进行了比较。迄今为止,英文出版物中尚未报道原发性干燥综合征合并肺动脉高压的病例。这三例病例表明,原发性干燥综合征合并肺动脉高压的情况虽不常见,但应纳入临床谱范畴。