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右位心伴内脏转位患者的应激性心肌病

Takotsubo Cardiomyopathy in Dextrocardia with Situs Inversus.

作者信息

Ganes A, Segan L

机构信息

Department of Cardiology, Barwon Health, Bellerine Street, Geelong, VIC 3220, Australia.

出版信息

Case Rep Cardiol. 2020 Aug 20;2020:8844691. doi: 10.1155/2020/8844691. eCollection 2020.

DOI:10.1155/2020/8844691
PMID:32884846
原文链接:https://pmc.ncbi.nlm.nih.gov/articles/PMC7455845/
Abstract

Takotsubo cardiomyopathy (TTC) is an acute reversible form of left ventricular (LV) systolic dysfunction extending beyond a coronary artery vascular territory usually due to physical or psychological stressors. Dextrocardia with situs inversus is a rare embryologic anomaly whereby the heart and aorta are mirrored on the contralateral side. We describe a case of a 93-year-old female with dextrocardia who presented with chest pain, atrial fibrillation with rapid ventricular response, and transient inferior ST elevation. Coronary angiography demonstrated an eccentric mid right coronary artery (RCA) lesion and apical ballooning consistent with concurrent takotsubo cardiomyopathy (TTC). To our knowledge, this is the first reported case of this dual pathology in a patient with dextrocardia, highlighting the procedural and diagnostic complexity in the setting of a rare anatomicvariant.

摘要

应激性心肌病(TTC)是一种急性可逆性左心室(LV)收缩功能障碍,通常由于身体或心理应激源导致其范围超出冠状动脉血管区域。右位心伴内脏转位是一种罕见的胚胎学异常,心脏和主动脉在对侧呈镜像。我们描述了一例93岁右位心女性患者,其表现为胸痛、快速心室率的心房颤动以及短暂性下壁ST段抬高。冠状动脉造影显示右冠状动脉(RCA)中段偏心病变和心尖部气球样变,符合同时存在应激性心肌病(TTC)。据我们所知,这是首例报道的右位心患者出现这种双重病理情况的病例,凸显了在罕见解剖变异情况下的操作和诊断复杂性。

https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8a0f/7455845/8adde0a39df7/CRIC2020-8844691.003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8a0f/7455845/b05eb60c0ff9/CRIC2020-8844691.001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8a0f/7455845/10c32e189ec9/CRIC2020-8844691.002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8a0f/7455845/8adde0a39df7/CRIC2020-8844691.003.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8a0f/7455845/b05eb60c0ff9/CRIC2020-8844691.001.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8a0f/7455845/10c32e189ec9/CRIC2020-8844691.002.jpg
https://cdn.ncbi.nlm.nih.gov/pmc/blobs/8a0f/7455845/8adde0a39df7/CRIC2020-8844691.003.jpg

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本文引用的文献

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A Rare Case of Takotsubo Syndrome and Acute Coronary Syndrome of the Right Coronary Artery.一例罕见的应激性心肌病合并右冠状动脉急性冠状动脉综合征
Case Rep Cardiol. 2019 Jun 9;2019:9128273. doi: 10.1155/2019/9128273. eCollection 2019.
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Eur Heart J. 2018 Jun 7;39(22):2047-2062. doi: 10.1093/eurheartj/ehy077.
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