Monfort-Gouraud M, Sinnassamy P, Bensman A, Sirinelli D, Boccon-Gibod L
Service de Radiologie et du Laboratoire d'Anatomie-Pathologie, Hôpital Trousseau, Paris.
Arch Fr Pediatr. 1988 Feb;45(2):129-31.
In the most common clinical expression of infantile polycystic disease, the kidneys are greatly enlarged in the neonatal period. When the child gets older the kidneys become smaller. In this case report, both kidneys kept growing after birth causing abdominal distention and respiratory distress. The differential diagnosis was a bilateral massive nephroblastomatosis, but the renal pathology showed characteristic features of infantile polycystic disease.
在婴儿多囊病最常见的临床症状中，新生儿期肾脏会显著增大。随着孩子长大，肾脏会变小。在本病例报告中，双侧肾脏在出生后持续生长，导致腹胀和呼吸窘迫。鉴别诊断为双侧巨大肾母细胞瘤病，但肾脏病理显示为婴儿多囊病的特征性表现。
