Internal Medicine "B" Department, Rambam Health Care Campus, Haifa, Israel.
Pathology Institute, Rambam Health Care Campus, Haifa, Israel; Ruth and Bruce Rappaport Faculty of Medicine, Technion, Haifa, Israel.
Pathol Res Pract. 2020 Nov;216(11):153209. doi: 10.1016/j.prp.2020.153209. Epub 2020 Sep 10.
Castleman disease is a rare lymphoproliferative disorder presenting frequently with constitutional symptoms. Although pleural effusion is common, there is only one case report of an adult patient with chylous pleural effusion. We present the first case report of a hypervascular variant of Castleman disease presenting as a chylous pleural effusion and successfully treated with a combination of anti-interleukin-6 agent and steroids.
卡斯尔曼病是一种罕见的淋巴组织增生性疾病，常伴有全身症状。尽管胸腔积液很常见，但仅有一例成人乳糜性胸腔积液的病例报告。我们报告首例表现为乳糜性胸腔积液的高血管变异型卡斯尔曼病，并成功地采用抗白细胞介素-6 制剂和类固醇联合治疗。
