From the Department of Nuclear Medicine, Marmara University Pendik Training and Research Hospital, Istanbul, Turkey.
Department of Pathology, Marmara University Pendik Training and Research Hospital, Istanbul, Turkey.
Clin Nucl Med. 2021 Jan;46(1):86-87. doi: 10.1097/RLU.0000000000003297.
Extrarenal Wilms tumor (ERWT) is an extremely rare neoplasm of childhood. It occurs predominantly in retroperitoneum and pelvic or inguinal region without involvement of the kidneys. Although the importance of FDG PET/CT in Wilms tumor is well known, its use in ERWT is limited. Herein, we present FDG PET/CT findings of a 3-year-old girl with a lumbar mass, which was later diagnosed with ERWT.
肾外 Wilms 瘤(ERWT)是一种极为罕见的儿童期肿瘤。它主要发生在腹膜后和骨盆或腹股沟区域,而不涉及肾脏。虽然 FDG PET/CT 在 Wilms 瘤中的重要性众所周知,但在 ERWT 中的应用有限。在此,我们介绍了一名 3 岁女孩腰部肿块的 FDG PET/CT 发现,该女孩后来被诊断为 ERWT。