Jayasinghe Dinesha Ruwanthi, Dissanayake Karuna, de Silva Mannikawadumesthri Vipula Chandu
Department of Pathology, Faculty of Medicine, University of Colombo, Colombo, Sri Lanka.
Department of Pathology, National Hospital of Sri Lanka, Colombo, Sri Lanka.
J Cutan Pathol. 2021 Apr;48(4):486-494. doi: 10.1111/cup.13882. Epub 2020 Oct 29.
Mycosis fungoides (MF), the commonest primary cutaneous T-cell lymphoma, has classic and variant types which include hypopigmented MF (HMF). Previous studies have identified distinct clinicopathological profiles in HMF. This study aims to objectively compare the clinicopathological features of HMF with non-HMF lesions in order to characterize salient features of HMF.
This cross-sectional, retrospective study analyzed biopsy specimens of 87 patients with MF. HMF and non-HMF groups were compared using clinical data, immunophenotypic features and scores given for six histopathological features: dermal infiltrate, basilar and superficially extending epidermotropism, Pautrier microabscesses and dermal and epidermotropic lymphocytic atypia.
Seventy-six patients had HMF. Presentation in females (59.21%; p = .04) and patch stage (88.16%; p = .01) in HMF were significant, and HMF presented at a younger mean age when compared to non-HMF. Both groups had equal intensity of epidermotropism, with HMF showing milder dermal infiltrates and significantly less dermal atypia. Pautrier microabscesses were significantly commoner in non-HMF (LR 10.76; p < .01). 94.74% of HMF were CD4-/CD8+.
HMF presents at a lower age and earlier stage with female predominance compared to non-HMF. Because of milder dermal infiltrates, less dermal atypia, and Pautrier microabscesses, the diagnosis of HMF requires correlation with clinical features and careful assessment of epidermotropic cells.
蕈样肉芽肿(MF)是最常见的原发性皮肤T细胞淋巴瘤,有经典型和变异型,其中包括色素减退性蕈样肉芽肿(HMF)。既往研究已确定HMF具有独特的临床病理特征。本研究旨在客观比较HMF与非HMF皮损的临床病理特征,以明确HMF的显著特征。
这项横断面回顾性研究分析了87例MF患者的活检标本。使用临床数据、免疫表型特征以及针对六种组织病理学特征给出的评分(真皮浸润、基底及浅表性表皮内亲表皮性、Pautrier微脓肿以及真皮和表皮内亲表皮性淋巴细胞异型性)对HMF组和非HMF组进行比较。
76例患者患有HMF。HMF在女性中的发病率(59.21%;p = 0.04)及斑块期发病率(88.16%;p = 0.01)具有统计学意义,且与非HMF相比,HMF的平均发病年龄更小。两组的表皮内亲表皮性强度相同,HMF的真皮浸润较轻,真皮异型性明显较少。Pautrier微脓肿在非HMF中明显更常见(似然比10.76;p < 0.01)。94.74%的HMF为CD4-/CD8+。
与非HMF相比,HMF发病年龄更低、分期更早,且以女性为主。由于真皮浸润较轻、真皮异型性较少以及Pautrier微脓肿较少,HMF的诊断需要结合临床特征并仔细评估表皮内亲表皮性细胞。