Youssef Randa, Mahgoub Doaa, Zeid Ola A, Abdel-Halim Dalia M, El-Hawary Marwa, Hussein Marwa F, Morcos Mary A, Aboelfadl Dalia M, Abdelkader Heba A, Abdel-Galeil Yosra, Abdel-Halim Mona R E
Dermatology Department, Cairo University, Cairo, Egypt.
Histology Department, Cairo University, Cairo, Egypt.
Am J Dermatopathol. 2018 Oct;40(10):727-735. doi: 10.1097/DAD.0000000000001187.
Hypopigmented interface T-cell dyscrasia (HITCD) is a distinct form of lymphoid dyscrasia that may progress to hypopigmented mycosis fungoides (HMF). We compared both diseases as regards their CD4/CD8 phenotype and expression of granzyme B and tumor necrosis factor-alpha (TNF-α) and how these are affected by narrow-band UVB (nb-UVB). The study included 11 patients with HITCD and 9 patients with HMF. They received nb-UVB thrice weekly until complete repigmentation or a maximum of 48 sessions. Pretreatment and posttreatment biopsies were stained using anti CD4, CD8, TNF-α, and granzyme B monoclonal antibodies. Epidermal lymphocytes were CD8 predominant in 54.5% and 66.7% of HITCD and HMF cases, respectively, whereas dermal lymphocytes were CD4 predominant in 63.6% and 66.7%, respectively. Significantly, more dermal infiltrate was encountered in HMF (P = 0.041). In both diseases, granzyme B was only expressed in the dermis, whereas TNF-α was expressed both in the epidermis and dermis. No difference existed as regards the number of sessions needed to achieve repigmentation or cumulative nb-UVB dose reached at end of study. (P > 0.05). Narrow-band UVB significantly reduced only the epidermal lymphocytes in both diseases (P ≤ 0.05) with their complete disappearance in 8 (72.7%) HITCD and 6 (66.7%) HMF cases. In both diseases, nb-UVB did not affect granzyme B or TNF-α expression (P > 0.05). In conclusion, both diseases share the same phenotype, with HITCD being a milder form of T-cell dysfunction. In both diseases, epidermal lymphocytes are mainly CD8-exhausted cells lacking cytotoxicity, whereas dermal cells are mostly reactive cells exerting antitumor cytotoxicity. Tumor necrosis factor-alpha mediates hypopigmentation in both diseases and prevents disease progression. Repigmentation after nb-UVB in both diseases occurs before and independently from disappearance of the dermal infiltrate.
色素减退性界面T细胞发育异常(HITCD)是一种独特的淋巴样发育异常形式,可能进展为色素减退性蕈样肉芽肿(HMF)。我们比较了这两种疾病的CD4/CD8表型、颗粒酶B和肿瘤坏死因子-α(TNF-α)的表达情况,以及窄谱中波紫外线(nb-UVB)对它们的影响。该研究纳入了11例HITCD患者和9例HMF患者。他们每周接受3次nb-UVB照射,直至完全复色或最多照射48次。治疗前和治疗后的活检组织使用抗CD4、CD8、TNF-α和颗粒酶B单克隆抗体进行染色。在HITCD和HMF病例中,分别有54.5%和66.7%的表皮淋巴细胞以CD8为主,而在真皮淋巴细胞中,分别有63.6%和66.7%以CD4为主。值得注意的是,HMF中的真皮浸润更明显(P = 0.041)。在这两种疾病中,颗粒酶B仅在真皮中表达,而TNF-α在表皮和真皮中均有表达。在实现复色所需的照射次数或研究结束时达到的累积nb-UVB剂量方面,两者没有差异(P > 0.05)。窄谱中波紫外线仅显著减少了这两种疾病中的表皮淋巴细胞(P≤0.05),在8例(72.7%)HITCD和6例(66.7%)HMF病例中表皮淋巴细胞完全消失。在这两种疾病中,nb-UVB均未影响颗粒酶B或TNF-α的表达(P > 0.05)。总之,这两种疾病具有相同的表型,HITCD是一种较轻形式的T细胞功能障碍。在这两种疾病中,表皮淋巴细胞主要是缺乏细胞毒性的CD8耗竭细胞,而真皮细胞大多是发挥抗肿瘤细胞毒性的反应性细胞。肿瘤坏死因子-α在这两种疾病中均介导色素减退并阻止疾病进展。两种疾病经nb-UVB治疗后的复色发生在真皮浸润消失之前且与之无关。