Department of Radiology, Silhouette Diagnostic Consultants, Abuja, Nigeria.
Department of Radiology, Children's Hospital of Philadelphia, Philadelphia, PA; Perelman School of Medicine at The University of Pennsylvania, Philadelphia, PA.
Semin Ultrasound CT MR. 2020 Oct;41(5):442-450. doi: 10.1053/j.sult.2020.05.009. Epub 2020 May 28.
The Fontan operation or the total cavopulmonary connection is a palliative surgery for single ventricle congenital heart disease where the systemic venous return circumvents a pumping chamber and flows directly into the pulmonary circuit. With surgical and medical advances, there has been improvement in life expectancy of these patients, however, it has also resulted in unique complications from the physiology that requires diligent surveillance. A critical component relies on optimal imaging for diagnosis and treatment of these complications. This article describes the normal anatomy of the Fontan circulation, current imaging modalities and techniques, and frequently encountered complications seen when imaging the patients who have undergone Fontan palliation.
法洛四联症手术或全腔肺动脉连接术是一种姑息性手术,用于治疗单心室先天性心脏病,其中体循环静脉回流绕过一个泵腔并直接流入肺循环。随着手术和医学的进步,这些患者的预期寿命有所提高,但也因此出现了独特的生理并发症,需要进行仔细监测。其中一个关键组成部分依赖于最佳的影像学诊断和治疗这些并发症。本文描述了法洛四联症循环的正常解剖结构、当前的成像方式和技术,以及在对接受法洛四联症姑息治疗的患者进行成像时经常遇到的并发症。